Heidari Zahra, Kaykhaei Mahmoud Ali, Jahantigh Mahdi, Sheikhi Vahid
Department of Endocrinology and Metabolism, Zahedan University of Medical Sciences, Zahedan, Iran.
Department of Pathology, Zahedan University of Medical Sciences, Zahedan, Iran.
Int J Endocrinol Metab. 2018 Jan 10;16(1):e63055. doi: 10.5812/ijem.63055. eCollection 2018 Jan.
Ganglioneuroblastoma is a primary malignant tumor of the sympathetic nervous system. It usually occurs in children and is extremely rare in adults. Here, we report a case of an adrenal ganglioneuroblastoma in a 38-year-old man. The adrenal incidentaloma was surgically removed and pathologically diagnosed as a ganglioneuroblastoma. The characteristics were described, because it is an unusual tumor based on the published reports in adults. To the best of our knowledge, fewer than 50 cases of ganglioneuroblastoma and 19 cases of adrenal ganglioneuroblastoma, including this case, are reported in the literature.
神经节神经母细胞瘤是交感神经系统的原发性恶性肿瘤。它通常发生于儿童，在成人中极为罕见。在此，我们报告一例38岁男性肾上腺神经节神经母细胞瘤病例。该肾上腺偶发瘤经手术切除，病理诊断为神经节神经母细胞瘤。鉴于根据已发表的成人病例报告，这是一种不常见的肿瘤，故对其特征进行了描述。据我们所知，文献报道的神经节神经母细胞瘤病例少于50例，包括本病例在内的肾上腺神经节神经母细胞瘤病例为19例。
