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成人线状IgA大疱性皮肤病:三例报告

Adult linear IgA bullous dermatosis: report of three cases.

作者信息

Machado Taila Yuri Siqueira, Enokihara Milvia Maria Simões E Silva, Iida Tatiana Miyuki, Porro Adriana Maria

机构信息

Department of Dermatology, Escola Paulista de Medicina, Universidade Federal de São Paulo, São Paulo, SP, Brasil.

出版信息

An Bras Dermatol. 2018 Jun;93(3):435-437. doi: 10.1590/abd1806-4841.20187304.

Abstract

Linear immunoglobulin A bullous dermatosis is a rare autoimmune disease that usually has an excellent prognosis in childhood; however, its control is more difficult in adults. It presents heterogeneous clinical manifestations and is frequently confused with other bullous diseases such as bullous pemphigoid and Duhring's dermatitis herpetiformis. Dermatologists' awareness of this disease contributes to early diagnosis and appropriate treatment. We thus report three cases of linear immunoglobulin A dermatosis in adults.

摘要

线状免疫球蛋白A大疱性皮肤病是一种罕见的自身免疫性疾病,在儿童期通常预后良好;然而,在成人中对其进行控制则更为困难。它表现出异质性的临床表现,并且经常与其他大疱性疾病如大疱性类天疱疮和杜林疱疹样皮炎相混淆。皮肤科医生对这种疾病的认识有助于早期诊断和恰当治疗。因此,我们报告三例成人线状免疫球蛋白A皮肤病病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3e33/6001096/649a67931757/abd-93-03-0435-g01.jpg

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