Couvreur Thierry, Lipcsei Györgyi, Nchimi Alain
Department of Medical Imaging, University Hospital-Sart Tilman, Liège, Belgium.
Department of Pathology, CHC-St Joseph, Liège, Belgium.
Aorta (Stamford). 2013 Jul 1;1(2):146-148. doi: 10.12945/j.aorta.2013.13-023. eCollection 2013 Jul.
Reaching etiologic diagnoses for retroperitoneal fibrosis may be challenging. We report the case of a 75-year old male with history of ruptured abdominal aortic aneurysm and subsequent retroperitoneal fibrosis who developed four years later a soft tissue infiltration surrounding the ascending thoracic aorta. Thanks to his medical records and multimodality imaging assessment, the patient escaped an open-chest biopsy through histolgical reassessment of the abdominal periaortic samples that allowed the definitive diagnosis of Erdheim-Chester disease, a rare non-Langerhans histiocytosis.
明确腹膜后纤维化的病因诊断可能具有挑战性。我们报告了一例75岁男性病例，该患者有腹主动脉瘤破裂病史，随后发生腹膜后纤维化，四年后出现胸段升主动脉周围软组织浸润。得益于其病历和多模态影像学评估，通过对腹主动脉周围样本进行组织学重新评估，患者避免了开胸活检，从而明确诊断为 Erdheim-Chester 病，这是一种罕见的非朗格汉斯组织细胞增多症。
