Surya Mukesh, Thakur Sita, Singh Kamal, Soni Pawan, Sood Dinesh, Kapila Preeti Takkar
Department of Radiodiagnosis, DRPGMC Kangra at Tanda, Kangra, India.
Department of Obstetrics & Gynaecology, DRPGMC Kangra at Tanda, Kangra, India.
BJR Case Rep. 2016 Feb 25;2(2):20150241. doi: 10.1259/bjrcr.20150241. eCollection 2016.
Obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) is an unusual and special type of Müllerian duct anomaly. Patients usually present in adolescence, soon after menarche, with pain and pelvic mass and rarely with infertility in adulthood. Majority of the cases of OHVIRA have been reported in association with uterus didelphys and the presentation of uterus didelphys with OHVIRA is known as Herlyn-Werner-Wunderlich syndrome. A complete septate uterus with OHVIRA is exceedingly unusual. Less than 30 cases of complete septate uterus with OHVIRA have been reported to date, to the best of our knowledge. We present a rare case of incidentally detected complete septate uterus with OHVIRA in a young woman who presented with acute pain in the right iliac fossa owing to acute appendicitis.
梗阻性半阴道并同侧肾缺如（OHVIRA）是一种罕见且特殊类型的苗勒管发育异常。患者通常在青春期、月经初潮后不久出现疼痛和盆腔肿块，成年后很少出现不孕。大多数OHVIRA病例报告与双子宫相关，双子宫合并OHVIRA的表现被称为赫林 - 韦纳 - 温德利希综合征。完全纵隔子宫合并OHVIRA极为罕见。据我们所知，迄今为止报道的完全纵隔子宫合并OHVIRA病例不足30例。我们报告了一例罕见病例，一名年轻女性因急性阑尾炎出现右下腹急性疼痛，偶然发现其患有完全纵隔子宫合并OHVIRA。
