Bezabih Natnael Alemu, Mehammed Abdudin Heru, Gebresilassie Muluken Yifru, Regasa Nebiyu Damtew
Addis Ababa University, College of Health Sciences, Department of Radiology, Addis Ababa, Ethiopia.
Saint Paul's Hospital, Millennium Medical College, Department of Radiology, Addis Ababa, Ethiopia.
Radiol Case Rep. 2024 Jun 15;19(9):3667-3671. doi: 10.1016/j.radcr.2024.05.076. eCollection 2024 Sep.
Obstructed hemivagina and ipsilateral renal anomaly syndrome (OHVIRA) also known as Herlyn-Werner-Wunderlich syndrome is a rare type of Müllerian duct anomaly with concomitant mesonephric duct anomalies. It is characterized by uterus didelphys, obstructed hemi-vagina, and commonly renal agenesis however; other types of mesonephric duct anomalies such as duplicated kidneys, dysplastic kidneys, rectovesical bands, or crossed fused ectopia have also been reported. We present a case report of a 21-year-old female patient experiencing new-onset vaginal bleeding and pelvic pain over the past month. Subsequent multi-sequence MRI revealed characteristic features indicative of OHVIRA syndrome. Clinical manifestations typically encompass pelvic pain and menstrual abnormalities but mainly depend upon the presence of communication between the hemi-uterus. This article aims to discuss the clinical presentation, types, and diagnostic utility of ultrasound and MRI in OHVIRA syndrome. Additionally, we discuss the possible management plans.
梗阻性半阴道及同侧肾异常综合征（OHVIRA），也称为赫林 - 韦纳 - 温德利希综合征，是一种罕见的苗勒管异常类型，并伴有中肾管异常。其特征为双子宫、半阴道梗阻，通常还伴有肾缺如；不过，也有报道称存在其他类型的中肾管异常，如重复肾、发育异常肾、直肠膀胱带或交叉融合异位肾。我们报告一例21岁女性患者病例，该患者在过去一个月出现新发阴道出血和盆腔疼痛。随后的多序列磁共振成像（MRI）显示出指示OHVIRA综合征的特征性表现。临床表现通常包括盆腔疼痛和月经异常，但主要取决于半子宫之间是否存在连通。本文旨在探讨OHVIRA综合征的临床表现、类型以及超声和MRI的诊断效用。此外，我们还讨论了可能的治疗方案。
