Gregory Fleming James Cystic Fibrosis Research Center Birmingham, AL, USA; The Department of Medicine, University of Alabama at Birmingham Birmingham, AL, USA.
Gregory Fleming James Cystic Fibrosis Research Center Birmingham, AL, USA; The Department of Medicine, University of Alabama at Birmingham Birmingham, AL, USA.
J Cyst Fibros. 2019 Mar;18(2):e11-e13. doi: 10.1016/j.jcf.2018.11.013. Epub 2018 Nov 29.
To raise awareness of colocolonic intussusception as a gastrointestinal complication of CF mimicking distal intestinal obstruction syndrome (DIOS) and discuss risk of recurrence.
A 33-year-old Caucasian male with cystic fibrosis presented with an acute abdomen diagnosed via imaging as colocolonic intussusception. He was managed with fluid replacement therapy and polyethylene glycol. He was re-admitted due to recurrence likely secondary to recurrent constipation and development of a fecalith. Surgery was contraindicated due to absence of tissue ischemia or necrosis.
Several possible etiological factors have been described, especially some that tend to occur within the context of CF disease, such as DIOS and PERT, and symptoms of colocolonic intussusception are similar to those of other causes of an acute abdomen but distinguishable by advanced imaging modalities. Due to risk of recurrence, an etiology of intussusception should be sought.
Colo-colonic intussusception is a rare cause of an acute abdomen in the adult Cystic Fibrosis (CF) patient and may be associated with underlying constipation or presence of a fecalith.
提高对结肠结肠肠套叠作为 CF 的胃肠道并发症的认识，这种并发症类似于远端肠梗阻综合征（DIOS），并讨论其复发的风险。
一名 33 岁的白人男性，患有囊性纤维化，因急性腹痛就诊，影像学诊断为结肠结肠肠套叠。他接受了液体替代疗法和聚乙二醇治疗。由于反复出现的便秘和粪石形成，他可能再次发生了肠套叠，因此再次入院。由于没有组织缺血或坏死，手术被排除。
已经描述了几种可能的病因，特别是一些倾向于在 CF 疾病背景下发生的病因，如 DIOS 和 PERT，结肠结肠肠套叠的症状与其他急性腹痛的病因相似，但可以通过先进的成像方式来区分。由于存在复发的风险，应寻找肠套叠的病因。
结肠结肠肠套叠是成人囊性纤维化（CF）患者急性腹痛的罕见原因，可能与潜在的便秘或粪石存在有关。
