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利布曼-萨克斯心内膜炎中的肥厚性梗阻性心肌病和二尖瓣反流

Hypertrophic obstructive cardiomyopathy and mitral regurgitation in Libman-Sacks endocarditis.

作者信息

Yamashita Go, Kanemitsu Naoki, Nakashima Yasuaki, Matsuo Takehiko, Nakane Takeichiro, Honda Masanori, Okabayashi Hitoshi

机构信息

Department of Cardiovascular Surgery, Mitsubishi Kyoto Hospital, 1 Goshomachi, Nishikyo-ku, Kyoto, 615-8087, Japan.

Department of Pathology, Mitsubishi Kyoto Hospital, Kyoto, Japan.

出版信息

Gen Thorac Cardiovasc Surg. 2020 Feb;68(2):181-184. doi: 10.1007/s11748-018-1042-7. Epub 2018 Dec 5.

Abstract

Hypertrophic obstructive cardiomyopathy in Libman-Sacks endocarditis is quite rare and the correct etiological relationship between them is unknown. Some changes may cause a secondary disorganization of the ordinary muscle structure, making a disarray pattern with irregular interwoven myocyte fibers. This case report describes one of the first cases of ventricular septal myectomy and mitral valve replacement for hypertrophic obstructive cardiomyopathy and mitral valve regurgitation associated with Libman-Sacks endocarditis.

摘要

利布曼-萨克斯心内膜炎合并肥厚性梗阻性心肌病极为罕见,二者之间确切的病因关系尚不清楚。某些改变可能导致普通心肌结构继发性紊乱,形成肌细胞纤维不规则交织的紊乱模式。本病例报告描述了首例因利布曼-萨克斯心内膜炎合并肥厚性梗阻性心肌病及二尖瓣反流而接受室间隔心肌切除术和二尖瓣置换术的病例。

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