Subcorneal pustular dermatosis (Sneddon-Wilkinson disease) in association with a monoclonal IgA gammopathy: a report and review of the literature.

Subcorneal pustular dermatosis (Sneddon-Wilkinson disease) may be associated with a monoclonal gammopathy, most commonly an IgA paraproteinemia. This review looks at the available immunofluorescence staining data in the hope of finding a better characterization of this subset of patients and speculation as to the underlying pathophysiology.