对隐性营养不良性大疱性表皮松解症成人患者骨质疏松症的回顾性纵向研究。
Retrospective longitudinal study of osteoporosis in adults with recessive dystrophic epidermolysis bullosa.
作者信息
Hubbard Lynne D, Mayre-Chilton Kattya
机构信息
Department of Nutrition and Dietetics Guy's and St. Thomas' NHS Foundation Trust London UK.
出版信息
Clin Case Rep. 2018 Nov 12;7(1):58-63. doi: 10.1002/ccr3.1898. eCollection 2019 Jan.
Abstract
This retrospective study looks at bone mineral density of people with recessive dystrophic epidermolysis bullosa as assessed by dual-energy x-ray absorptiometry. Data were collected in 34 patients aged 16-35 years. Statistical analysis showed immobility, low body mass index, and pubertal delay was associated with osteoporosis.
摘要
这项回顾性研究通过双能X线吸收法评估了隐性营养不良型大疱性表皮松解症患者的骨矿物质密度。收集了34名年龄在16至35岁之间患者的数据。统计分析表明，活动不便、低体重指数和青春期延迟与骨质疏松症有关。
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