Ponomarev R V, Model S V, Zozulya N I, Ivanov V A, Podchasov D A, Mershina E A, Sinitsyn V E, Lukina E A
National Research Center for Hematology, Moscow, Russia.
Russian Scientific Center for Surgery named B.V. Petrovsky, Moscow, Russia.
Ter Arkh. 2018 Aug 17;90(7):86-90. doi: 10.26442/terarkh201890786-90.
Constrictive pericarditis (CP) is the final stage of a chronic inflammatory process characterized by fibrous thickening and calcification of the pericardium that impairs diastolic filling, reduces cardiac output, and ultimately leads to heart failure. We present a clinical case of CP in a patient with rare inherited bleeding disorder - factor VII deficiency. Heart failure due to CP was suspected based on clinical symptoms, results of ultrasonic and radiological investigations. The diagnosis was verified by the results of cardiac magnetic resonance imaging. Pericardectomy was performed resulting in significant improvement in the patient's condition.
缩窄性心包炎（CP）是一种慢性炎症过程的终末期，其特征为心包纤维增厚和钙化，损害舒张期充盈，降低心输出量，并最终导致心力衰竭。我们报告一例患有罕见遗传性出血性疾病——因子VII缺乏症患者的CP临床病例。基于临床症状、超声和放射学检查结果怀疑该患者因CP导致心力衰竭。心脏磁共振成像结果证实了诊断。进行心包切除术后患者病情显著改善。
