The Cyprus Institute of Neurology & Genetics, Bioinformatics Group, 6 International Airport Avenue, 2370 Nicosia, Cyprus, P.O.Box 23462, 1683, Nicosia, Cyprus.
The Cyprus School of Molecular Medicine, 6 International Airport Avenue, 2370 Nicosia, Cyprus, P.O.Box 23462, 1683, Nicosia, Cyprus.
Sci Rep. 2019 Mar 1;9(1):3266. doi: 10.1038/s41598-019-39796-w.
Variants of unknown/uncertain significance (VUS) pose a huge dilemma in current genetic variation screening methods and genetic counselling. Driven by methods of next generation sequencing (NGS) such as whole exome sequencing (WES), a plethora of VUS are being detected in research laboratories as well as in the health sector. Motivated by this overabundance of VUS, we propose a novel computational methodology, termed VariantClassifier (VarClass), which utilizes gene-association networks and polygenic risk prediction models to shed light into this grey area of genetic variation in association with disease. VarClass has been evaluated using numerous validation steps and proves to be very successful in assigning significance to VUS in association with specific diseases of interest. Notably, using VUS that are deemed significant by VarClass, we improved risk prediction accuracy in four large case-studies involving disease-control cohorts from GWAS as well as WES, when compared to traditional odds ratio analysis. Biological interpretation of selected high scoring VUS revealed interesting biological themes relevant to the diseases under investigation. VarClass is available as a standalone tool for large-scale data analyses, as well as a web-server with additional functionalities through a user-friendly graphical interface.
未知/不确定意义的变异(VUS)在当前的遗传变异筛选方法和遗传咨询中构成了巨大的困境。在下一代测序(NGS)方法的推动下,如外显子组测序(WES),大量的 VUS 不仅在研究实验室中,而且在卫生部门也被检测到。受 VUS 大量出现的启发,我们提出了一种新的计算方法,称为 VariantClassifier(VarClass),它利用基因关联网络和多基因风险预测模型,揭示与疾病相关的遗传变异的这一灰色地带。VarClass 已经通过多种验证步骤进行了评估,并且在与特定疾病相关的 VUS 分类方面非常成功。值得注意的是,使用 VarClass 认为有意义的 VUS,与传统的优势比分析相比,我们在涉及来自 GWAS 和 WES 的疾病对照队列的四个大型案例研究中提高了风险预测准确性。对选定的高得分 VUS 的生物学解释揭示了与研究疾病相关的有趣生物学主题。VarClass 可作为大规模数据分析的独立工具,也可作为具有通过用户友好的图形界面提供附加功能的网络服务器。