Hilton A M, Doyle L
Br J Dis Chest. 1978 Jul;72(3):207-16. doi: 10.1016/0007-0971(78)90043-8.
Fifty-three patients with bronchiectasis (chronic bronchial suppuration) of unknown cause, in whom the chronic production of purulent sputum was the prominent clinical feature, were investigated for possible immunological abnormalities. They were compared with two control groups comprising 50 patients with chronic bronchitis and emphysema and 33 patients with bronchial asthma. Forty-two patients with bronchiectasis(79%) had at least one abnormality of immunoglobulin, usually elevation of IgA, IgG or IgM. Eight patients had all three immunoglobulin levels raised and this was related to severity of disease. Similar increases in immunoglobulin levels were observed in the control groups, but the frequency and severity of these changes were significantly greater in the bronchiectasis patients. Two patients had IgA deficiency. There was a very high prevalence of rheumatoid factor (52%) and an increased prevalence of antinuclear factor (10%) in the bronchiectasis patients compared with the control groups. The presence of these autoantibodies did not correlate closely with severity of disease. Ten patients with bronchiectasis (19%) had one or more autoimmune disorders, and the association of severe bronchiectasis, Hashimoto's thyroiditis and pernicious anaemia in one patient is described in detail. The immunoglobulin changes, high incidence of autoantibodies and association with autoimmune disorders raises the possibility that in some patients with bronchiectasis (chronic bronchial suppuration) of apparent unknown cause abnormal immune mechanisms may be important in causing or perpetuating the condition.
对53例病因不明的支气管扩张症(慢性支气管化脓症)患者进行了研究,这些患者以长期咳出脓性痰为主要临床特征,旨在探寻可能存在的免疫异常情况。将他们与两个对照组进行比较,其中一个对照组有50例慢性支气管炎和肺气肿患者,另一个对照组有33例支气管哮喘患者。42例支气管扩张症患者(79%)至少存在一种免疫球蛋白异常,通常是IgA、IgG或IgM升高。8例患者的三种免疫球蛋白水平均升高,且这与疾病严重程度相关。在对照组中也观察到免疫球蛋白水平有类似升高,但这些变化在支气管扩张症患者中的发生频率和严重程度明显更高。2例患者存在IgA缺乏。与对照组相比,支气管扩张症患者中类风湿因子的患病率非常高(52%),抗核因子的患病率也有所增加(10%)。这些自身抗体的存在与疾病严重程度并无密切关联。10例支气管扩张症患者(19%)患有一种或多种自身免疫性疾病,并详细描述了1例患者同时患有严重支气管扩张症、桥本甲状腺炎和恶性贫血的情况。免疫球蛋白变化、自身抗体的高发病率以及与自身免疫性疾病的关联提示,在一些病因明显不明的支气管扩张症(慢性支气管化脓症)患者中,异常免疫机制可能在导致或使病情持续方面起重要作用。