Department of Dermatology, Tampere University Hospital, Tampere, Finland; Celiac Disease Research Center, Tampere University, Faculty of Medicine and Health Technology, Tampere, Finland.
Celiac Disease Research Center, Tampere University, Faculty of Medicine and Health Technology, Tampere, Finland; Department of Internal Medicine, Tampere University Hospital, Tampere, Finland.
J Invest Dermatol. 2019 Oct;139(10):2108-2114. doi: 10.1016/j.jid.2019.03.1150. Epub 2019 Apr 15.
Dermatitis herpetiformis (DH) is an extraintestinal manifestation of celiac disease causing an itchy, blistering rash. Granular IgA deposits in the skin are pathognomonic for DH, and the treatment of choice is a lifelong gluten-free diet (GFD). Preliminary evidence suggests that there are patients with DH who redevelop gluten tolerance after adherence to a GFD treatment. To evaluate this, we performed a 12-month gluten challenge with skin and small-bowel mucosal biopsy samples in 19 patients with DH who had adhered to a GFD for a mean of 23 years. Prechallenge biopsy was negative for skin IgA and transglutaminase 3 deposits in 16 patients (84%) and indicated normal villous height-to-crypt depth ratios in the small bowel mucosa in all 19 patients. The gluten challenge caused a relapse of the rash in 15 patients (79%) in a mean of 5.6 months; of these 15 patients, 13 had skin IgA and transglutaminase 3 deposits, and 12 had small-bowel villous atrophy. In addition, three patients without rash or immune deposits in the skin developed villous atrophy, whereas one patient persisted without any signs of relapse. In conclusion, 95% of the patients with DH were unable to tolerate gluten even after long-term adherence to a GFD. Therefore, lifelong GFD treatment remains justified in all patients with DH.
疱疹样皮炎(DH)是一种胃肠道外的乳糜泻表现,会导致瘙痒、水疱样皮疹。皮肤中颗粒状 IgA 沉积是 DH 的特征性表现,治疗选择是终生无麸质饮食(GFD)。初步证据表明,有些 DH 患者在坚持 GFD 治疗后会重新获得对麸质的耐受性。为了评估这一点,我们对 19 例坚持 GFD 治疗平均 23 年的 DH 患者进行了为期 12 个月的麸质挑战,并进行了皮肤和小肠黏膜活检。16 例患者(84%)的预挑战活检皮肤 IgA 和转谷氨酰胺酶 3 沉积均为阴性,19 例患者的小肠黏膜绒毛高度与隐窝深度比值均正常。麸质挑战导致 15 例患者(79%)平均 5.6 个月后皮疹复发;这 15 例患者中,13 例皮肤 IgA 和转谷氨酰胺酶 3 沉积阳性,12 例小肠绒毛萎缩。此外,3 例无皮疹或皮肤免疫沉积物的患者出现绒毛萎缩,而 1 例患者持续无任何复发迹象。总之,95%的 DH 患者即使长期坚持 GFD 也无法耐受麸质。因此,终身 GFD 治疗仍然是所有 DH 患者的合理选择。