Leijala M, Louhimo I
Prog Pediatr Surg. 1987;21:98-106. doi: 10.1007/978-3-642-71665-2_13.
Sixteen patients with extralobar sequestration of the lung are reported on. The age at time of diagnosis varied from 21 days to 12 years (mean 3.6 years). Most of the patients presented with respiratory symptoms, such as dyspnoea, pneumonia, coughing attacks, cyanosis and asthmatic symptoms, but diagnosis was made incidentally in 4. Diagnosis was established by chest X-ray in every case. Preoperative angiography and bronchography was carried out in six cases. All 16 patients underwent thoracotomy for removal of the sequestration. Rudimentary bronchial remnants were found in 6 cases. Extralobar sequestration was associated with 12 additional malformations in 10 of the 16 patients. The clinical picture varies considerably and many of the "typical" features, such as systemic arterial blood supply, left lower lobe localization and diaphragmatic defect, are often absent. Diagnosis and treatment are easy.
本文报道了16例肺叶外型肺隔离症患者。诊断时的年龄从21天至12岁不等（平均3.6岁）。大多数患者表现出呼吸症状，如呼吸困难、肺炎、咳嗽发作、发绀和哮喘症状，但有4例是偶然诊断出来的。所有病例均通过胸部X线确诊。6例患者术前行血管造影和支气管造影。所有16例患者均接受了开胸手术以切除隔离肺。6例发现有残留的支气管残端。16例患者中有10例的肺叶外型肺隔离症合并另外12种畸形。临床表现差异很大，许多“典型”特征，如体循环动脉供血、左下叶定位和膈肌缺损，往往并不存在。诊断和治疗都很容易。
