Ozkok Sercin, Erol Nurdan, Onal Canver, Yikilmaz Ali
Department of Radiology, Istanbul Medeniyet University Goztepe Training and Research Hospital, Istanbul, Turkey.
Department of Peadiatric Cardiology, Istanbul Medeniyet University Goztepe Training and Research Hospital, Istanbul, Turkey.
North Clin Istanb. 2018 Sep 3;6(2):192-195. doi: 10.14744/nci.2018.82698. eCollection 2019.
Poland's syndrome is a rare congenital anomaly accompanied by the absence of the pectoralis major, and the ipsilateral upper-limb and chest wall deformities. Hypoplasia of the breast, agenesis of the ipsilateral rib cartilage, athelia, and ipsilateral developmental finger anomalies such as syndactyly can also be seen. In the literature, only 56 cases of dextrocardia and left-sided Poland's syndrome have been described. Herein, a case of left-sided Poland's syndrome coexisting with dextrocardia and nasal hemangioma was presented.
波兰综合征是一种罕见的先天性异常,伴有胸大肌缺如以及同侧上肢和胸壁畸形。还可见乳房发育不全、同侧肋软骨发育不全、无乳头以及同侧发育性手指异常如并指等情况。在文献中,仅描述了56例右位心合并左侧波兰综合征的病例。在此,报告1例左侧波兰综合征合并右位心及鼻血管瘤的病例。