Cakmak Aslihan, Inal-Ince Deniz, Sonbahar-Ulu Hazal, Bozdemir-Ozel Cemile, Tekerlek Haluk, Saglam Melda, Calik-Kutukcu Ebru, Vardar-Yagli Naciye, Yalcin Elmas Ebru, Ozcelik Ugur, Arikan Hulya
Department of Physical Therapy and Rehabilitation, Hacettepe University, Ankara, Turkey.
Department of Pediatric Chest Medicine, Faculty of Medicine, Hacettepe University, Ankara, Turkey.
J Exerc Rehabil. 2019 Jun 30;15(3):468-471. doi: 10.12965/jer.1938144.072. eCollection 2019 Jun.
Kartagener's syndrome is a rare, autosomal recessive inherited disease, which is characterized by a triad of chronic sinusitis, bronchiectasis, and situs inversus. In this report, we aimed to represent the effect of aerobic exercise training in addition to chest physiotherapy in an outpatient with Kartagener's syndrome. An 18-year-old female diagnosed with Kartagener's syndrome applied with the complaints of productive cough and dyspnea with exertion and attended pulmonary rehabilitation program comprising exercise training in addition to standard treatment. Aerobic exercise training was performed three times weekly at 80% of the peak heart rate, for 8 weeks as supervised sessions. Respiratory physiotherapy and postural exercises were taught to the patient to be performed at home each day of the week. Before and after pulmonary rehabilitation program, incremental shuttle walk test (ISWT) was performed; dyspnea and fatigue were assessed using Borg Scale. Pulmonary function test was evaluated using spirometer. The patient wore activity monitor for 7 consecutive days before and after training. After pulmonary rehabilitation program, 90-m increase in ISWT was observed. We recommend exercise training in patients with Kartagener's syndrome to increase exercise capacity. Further randomized control trial is needed to clarify the effects.
卡塔格内综合征是一种罕见的常染色体隐性遗传病，其特征为慢性鼻窦炎、支气管扩张和内脏转位三联征。在本报告中，我们旨在阐述有氧运动训练联合胸部物理治疗对一名卡塔格内综合征门诊患者的效果。一名18岁被诊断为卡塔格内综合征的女性，因咳痰和劳力性呼吸困难前来就诊，并参加了包括运动训练及标准治疗的肺康复项目。有氧运动训练每周进行3次，强度为心率峰值的80%，在监督下进行8周。呼吸物理治疗和姿势训练教授给患者，让其每周在家中每天进行。在肺康复项目前后，进行递增式往返步行测试（ISWT）；使用Borg量表评估呼吸困难和疲劳程度。用肺活量计评估肺功能测试。患者在训练前后连续7天佩戴活动监测器。肺康复项目后，观察到ISWT增加了90米。我们建议对卡塔格内综合征患者进行运动训练以提高运动能力。需要进一步的随机对照试验来阐明其效果。
