Minocha Prashant K, Roop Lakhan, Persad Rambachan
Department of Paediatric Surgery, San Fernando General Hospital, Trinidad, Trinidad and Tobago.
Case Rep Pediatr. 2014;2014:626198. doi: 10.1155/2014/626198. Epub 2014 Sep 29.
Background. Lymphatic malformations or lymphangiomas are rare benign hamartomas that result from maldevelopment of primitive lymphatic sacs. They are most frequently found in the neck and axilla, while intra-abdominal and mediastinal lymphangiomas are uncommon. These are primarily tumours of infancy and childhood and are successfully treated with surgical excision. Summary of Cases. Five cases of lymphangioma comprising three intra-abdominal lymphangiomas and two unilateral axillary lymphangiomas presenting at one institution in Trinidad W.I. between 2005 and 2012 were examined. The presentations, location, workup, treatment, and outcome of these patients were studied. Conclusion. This paper discusses a range of extracervical lymphangioma cases seen at San Fernando General Hospital, Trinidad W.I. We report three intra-abdominal cases and the most common clinical presentations were abdominal pain and distension. Also two axillary cases were reported, which presented as painless axillary masses. The major concerns for excision of axillary lymphangioma by parents and surgeons were cosmesis and feasibility of complete resection without disruption of developing breast tissue and axillary vessels. We believe that ultrasound scan is very good at detection of the lesion, while CT is better at determining tumour content and planning for the operation. It is our opinion that complete surgical excision can be achieved.
背景。淋巴管畸形或淋巴管瘤是罕见的良性错构瘤,由原始淋巴囊发育异常引起。它们最常出现在颈部和腋窝,而腹腔内和纵隔淋巴管瘤并不常见。这些主要是婴幼儿期的肿瘤,手术切除可成功治疗。病例总结。对2005年至2012年间在特立尼达和多巴哥的一家机构就诊的5例淋巴管瘤病例进行了检查,其中包括3例腹腔内淋巴管瘤和2例单侧腋窝淋巴管瘤。对这些患者的临床表现、位置、检查、治疗及结果进行了研究。结论。本文讨论了在特立尼达和多巴哥圣费尔南多综合医院所见的一系列宫颈外淋巴管瘤病例。我们报告了3例腹腔内病例,最常见的临床表现是腹痛和腹胀。还报告了2例腋窝病例,表现为无痛性腋窝肿块。家长和外科医生对切除腋窝淋巴管瘤主要关注的是美观问题以及在不破坏发育中的乳腺组织和腋窝血管的情况下完整切除的可行性。我们认为超声扫描在检测病变方面非常有效,而CT在确定肿瘤内容物和手术规划方面更具优势。我们认为可以实现完整的手术切除。