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脊髓硬脊膜动静脉瘘所致进行性截瘫:一种罕见但可治疗的诊断,不应被漏诊。

Progressive Paraplegia Due to Spinal Dural Arteriovenous Fistula: A Rare but Treatable Diagnosis That Should Not Be Missed.

作者信息

Hameed Sajid, Taimuri Bushra, Sajid Marvi, Siraj Farah, Kamal Ayeesha

机构信息

Neurology, Aga Khan University, Karachi, PAK.

Anatomy, United Medical and Dental College, Karachi, PAK.

出版信息

Cureus. 2019 Oct 11;11(10):e5893. doi: 10.7759/cureus.5893.

DOI:10.7759/cureus.5893
PMID:31772863
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6837276/
Abstract

Spinal dural arteriovenous fistula (SDAVF) is the most common spinal vascular anomaly. It should always be considered in the differential diagnoses in a patient with progressive paraplegia or quadriplegia. We present a case of an elderly gentleman presenting with progressive paraplegia. The diagnosis was delayed as the previous physicians and radiologists missed the underlying key features of SDAVF on magnetic resonance imaging of the spine. Every neurologist and radiologist should be aware of these signs as SDAVF is mostly a treatable condition.

摘要

脊髓硬脊膜动静脉瘘(SDAVF)是最常见的脊髓血管畸形。对于出现进行性截瘫或四肢瘫的患者,在鉴别诊断时应始终考虑到该病。我们报告一例老年男性患者出现进行性截瘫的病例。由于之前的医生和放射科医生在脊柱磁共振成像上遗漏了SDAVF的关键特征,导致诊断延误。每位神经科医生和放射科医生都应了解这些体征,因为SDAVF大多是可治疗的疾病。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ac8/6837276/bc60f3d3d6a5/cureus-0011-00000005893-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ac8/6837276/77c64be04284/cureus-0011-00000005893-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ac8/6837276/bc60f3d3d6a5/cureus-0011-00000005893-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ac8/6837276/77c64be04284/cureus-0011-00000005893-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ac8/6837276/bc60f3d3d6a5/cureus-0011-00000005893-i02.jpg

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Spinal dural arteriovenous fistula: delay to radiological diagnosis and sources of radiological error.脊髓硬脊膜动静脉瘘:放射学诊断的延迟及放射学误诊原因
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脊髓动静脉分流:血管构筑与分类的历史变迁
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Spinal Dural Arteriovenous Fistula: A Review.脊髓硬脊膜动静脉瘘:综述
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