Ogbu Ikenna I, Tzerakis Nikolaos, Al-Shamary Zaineb
Department of Neurosurgery, Royal Stoke Hospital, University of North Midlands NHS Trust, Staffordshire, United Kingdom; and.
School of Medicine, Keele University, Staffordshire, United Kingdom.
J Neurosurg Case Lessons. 2021 Aug 30;2(9):CASE21283. doi: 10.3171/CASE21283.
Spinal dural arteriovenous fistulas (SDAVFs) are rare vascular malformations of the spine but account for up to 80% of all vascular malformations involving the spine. Few case reports of SDAVFs have been reported in the literature, and even fewer have been described with sudden onset of symptoms.
The authors described the case of a 72-year-old male with sudden-onset bilateral paraplegia and sensory loss with subsequent inability to bear weight and an initial suspicion of cauda equina syndrome, which was eventually diagnosed as an SDAVF using magnetic resonance imaging. During open surgery, it was difficult to identify the feeder vessels. A postoperative scan showed persistence of the fistula, and the patient had to receive redo ligation with good postoperative status.
Sudden-onset paraplegia is not the typical presentation of SDAVF. All doctors need to be aware of the possibility of an acute presentation with SDAVF, especially with the high likelihood of misdiagnosis and resultant worse outcome due to treatment delays. A high index of suspicion is required to ensure early recognition as well as initiation of treatment.
脊髓硬脊膜动静脉瘘(SDAVF)是一种罕见的脊柱血管畸形,但在所有累及脊柱的血管畸形中占比高达80%。文献中报道的SDAVF病例报告很少,症状突然发作的描述更是少之又少。
作者描述了一例72岁男性病例,该患者突然出现双侧截瘫和感觉丧失,随后无法承重,最初怀疑为马尾综合征,最终通过磁共振成像诊断为SDAVF。在开放手术中,很难识别供血血管。术后扫描显示瘘管持续存在,患者不得不接受再次结扎,术后恢复良好。
突然发作的截瘫并非SDAVF的典型表现。所有医生都需要意识到SDAVF急性发作的可能性,尤其是由于误诊和治疗延迟导致预后更差的可能性很大。需要高度怀疑指数以确保早期识别并开始治疗。