Moosa Safa Shaik, Hasan Hasan, Leyon Joe Joseph, Redha Noor Abdulla, Humaidan Hani
Salmaniya Medical Complex, Manama, Bahrain.
Department of Radiology, Salmaniya Medical Complex, Manama, Bahrain.
Radiol Case Rep. 2023 Sep 13;18(11):4123-4129. doi: 10.1016/j.radcr.2023.08.082. eCollection 2023 Nov.
Spinal dural arteriovenous fistulas (SDAVF) are the most common vascular malformations affecting the spinal cord. It is infrequently encountered in clinical practice and is believed to be acquired, predominantly affecting middle-aged and elderly men with unknown etiology. It is usually misdiagnosed despite presenting with conventional clinical findings and radiological features. Insidious onset of myelopathic findings is seen in addition to pathognomonic findings of cord edema and intrathecal flow voids on MRI. We present a case of SDAVF that was missed by the treating orthopedic surgeon and underwent spinal decompression with subsequent persistence of myelopathic symptoms. Angiography is required to confirm the diagnosis location of the fistula. Treatment is with embolization using liquid embolic agents or surgical through ligation of the draining vein. Endovascular techniques are minimally invasive, safe, and effective. Knowledge of the characteristics and advantages/disadvantages of each agent helps in planning and appropriate selection of agents for the patient. We report successful embolization with improved clinical outcomes for the patient using precipitating hydrophobic injectable liquid (PHIL) embolic agent. The outcome and prognosis of SDAVF depend on the duration of symptoms, severity of neurological symptoms, and successful occlusion of the fistulous draining vein. Awareness of this rare condition amongst clinicians and radiologists, would enable an earlier diagnosis and avoid morbid outcomes of this treatable condition.
脊髓硬脊膜动静脉瘘(SDAVF)是影响脊髓的最常见血管畸形。在临床实践中很少遇到,被认为是后天性的,主要影响中年和老年男性,病因不明。尽管具有传统的临床症状和影像学特征,但通常仍会被误诊。除了MRI上脊髓水肿和鞘内血流空洞的特征性表现外,还可见脊髓病症状的隐匿性发作。我们报告了一例SDAVF病例,该病例被主治骨科医生漏诊,接受了脊髓减压手术,但脊髓病症状持续存在。需要进行血管造影以确认瘘管的诊断位置。治疗方法是使用液体栓塞剂进行栓塞或通过结扎引流静脉进行手术。血管内技术微创、安全且有效。了解每种药物的特性和优缺点有助于为患者制定治疗方案并适当选择药物。我们报告了使用沉淀型疏水性可注射液体(PHIL)栓塞剂对患者进行成功栓塞并改善临床结果的情况。SDAVF的结果和预后取决于症状持续时间、神经症状的严重程度以及瘘管引流静脉的成功闭塞。临床医生和放射科医生对这种罕见疾病的认识,将有助于早期诊断并避免这种可治疗疾病的不良后果。