Ferreira Margarida S, Simões Joana, Folgado António, Carlos Sandra, Carvalho Nuno, Santos Filipa, Costa Paulo Matos
Department of General Surgery - Hospital Garcia de Orta, Avenida Torrado da Silva, 2805-267 Almada, Portugal; Faculdade de Medicina da Universidade de Lisboa, Avenida Professor Egas Moniz, 1649-028 Lisboa, Portugal.
Department of General Surgery - Hospital Garcia de Orta, Avenida Torrado da Silva, 2805-267 Almada, Portugal.
Int J Surg Case Rep. 2020;66:91-95. doi: 10.1016/j.ijscr.2019.11.037. Epub 2019 Nov 27.
Intestinal malrotation is a rare condition, with an incidence estimated between 0,2 to 1%. Most cases are diagnosed and treated during childhood. Adult presentations are rare and most adults present with chronic nonspecific complaints. Midgut volvulus is the most feared complication of intestinal malrotation, far more common among the pediatric than the adult population. Presentation in adulthood with a midgut volvulus accounts for a minority of these patients (15%). The Ladd procedure is the standard surgical management of midgut volvulus and intestinal malrotation. Most evidence on the outcomes of the Ladd procedure originates from studies on pediatric population and the recurrence among children who have had a Ladd procedure is low (2-7%).
We report an exceedingly rare case of a patient who presented in adulthood with a midgut volvulus and less than two years after undergoing Ladd procedure presented with a recurrence of the midgut volvulus. The recurrent midgut volvulus was successfully treated by a fixation procedure (cecopexy and duodenopexy).
Reports of midgut volvulus in adult patients are scarce and reports of recurrence even scarcer hence the rate of recurrence among adult patients has yet to be determined. The recurrence rate in some of the available adult series is much higher than the rate reported among children. Should the rate of recurrence among adult patients prove higher, it poses the question of whether the Ladd procedure should be modified to include bowel fixation when performed in adults.
肠旋转不良是一种罕见疾病,发病率估计在0.2%至1%之间。大多数病例在儿童期被诊断和治疗。成人发病情况罕见,大多数成人表现为慢性非特异性症状。中肠扭转是肠旋转不良最可怕的并发症,在儿科人群中比成人更常见。成年期出现中肠扭转的患者占少数(15%)。Ladd手术是中肠扭转和肠旋转不良的标准外科治疗方法。关于Ladd手术结果的大多数证据来自对儿科人群的研究,接受Ladd手术的儿童复发率较低(2%至7%)。
我们报告一例极其罕见的病例,一名成年患者出现中肠扭转,在接受Ladd手术后不到两年,中肠扭转复发。复发性中肠扭转通过固定手术(盲肠固定术和十二指肠固定术)成功治疗。
成人患者中肠扭转的报告很少,复发报告甚至更少,因此成人患者的复发率尚未确定。一些现有成人系列中的复发率远高于儿童报告的复发率。如果成人患者的复发率更高,就会引发一个问题,即在成人中进行Ladd手术时是否应修改手术方式以包括肠道固定。