Sussex Eye Hospital, Brighton.
National Specialist Ophthalmic Pathology Service (NSOPS), Dept of Histopathology, E-Floor, Royal Hallamshire Hospital Sheffield.
Ophthalmic Plast Reconstr Surg. 2020 Sep/Oct;36(5):438-443. doi: 10.1097/IOP.0000000000001589.
To describe 10 patients with Morbihan syndrome, a rare condition characterized by the slow appearance of erythema and solid edema on the upper portion of the face, and review the literature.
Retrospective case series and review.
The majority of patients were male (80%), and the mean age at presentation was 67 years (range, 48-88 years); 60% had asymmetrical disease (affecting mainly the right side). All subjects underwent a lid biopsy to support the diagnosis of Morbihan syndrome, which showed features of inflammation and vascular dysfunction, highly suggestive of a rosacea histological picture complicated by chronic lymphoedema. A range of medical and surgical treatment were used with variable success. The most effective ones included oral isotretinoin, intralesional triamcinolone injections, and debulking surgery.
Morbihan syndrome is a rare and chronic condition. It can be difficult to treat and may require a range of interventions.
描述 10 例 Morbihan 综合征患者，这是一种罕见的疾病，表现为面部上部缓慢出现红斑和坚实性水肿，并复习相关文献。
回顾性病例系列和综述。
大多数患者为男性（80%），发病时的平均年龄为 67 岁（范围，48-88 岁）；60%的患者疾病呈不对称性（主要影响右侧）。所有患者均接受了眼睑活检以支持 Morbihan 综合征的诊断，该诊断显示出炎症和血管功能障碍的特征，高度提示为伴有慢性淋巴水肿的酒渣鼻组织学图像。采用了一系列的药物和手术治疗，但疗效不一。最有效的治疗方法包括口服异维 A 酸、皮损内曲安奈德注射和减容手术。
Morbihan 综合征是一种罕见的慢性疾病，治疗较为困难，可能需要多种干预措施。
