Shamberger R C, Welch K J
Department of Surgery, Children's Hospital, Boston, MA 02115.
J Pediatr Surg. 1988 Jul;23(7):615-22. doi: 10.1016/s0022-3468(88)80629-8.
From 1958 to March 1987 we corrected 704 patients with pectus excavatum. The condition occurred more frequently in boys (544 patients) than girls (160 patients). In the majority of patients (86%), the defect was evident at birth or within the first year of life. Musculoskeletal abnormalities were identified in 133 patients (scoliosis, 107; kyphosis, 4; myopathy, 3; Poland's syndrome, 3; Marfan's syndrome, 2; Pierre Robin syndrome, 2; prune belly syndrome, 2; neurofibromatosis, 3; cerebral palsy, 4; tuberous sclerosis, 1; and congenital diaphragmatic hernia, 2). Sixteen patients had associated congenital heart disease. A family history of chest wall deformity was present in 37% of the cases and a history of scoliosis in 11%. Surgical correction was performed using a uniform technique for bilateral subperichondrial resection of the deformed costal cartilages and sternal osteotomy resecting a wedge of the anterior cortex and fracturing the posterior cortex. Anterior displacement was maintained with silk sutures closing the osteotomy defect. In 28 early cases, the sternum was secured by intramedullary fixation with a Steinman pin. All repairs were completed with a low complication rate (4.4%; pneumothorax, 11; wound infection, 5; wound hematoma, 3; wound dehiscence, 5; pneumonia, 3; seroma, 1; hemoptysis, 1; hemopericardium, 1). Six complications were associated with Steinman pin fixation (hemoptysis, seroma, hemopericardium, pneumothorax, 3). Major recurrence occurred in 17 patients (2.7%) and led to revision in 12. Satisfactory long-term results were achieved in the remaining 687 patients, with follow-up ranging from 2 weeks to 27 years. Mean follow-up was 4.3 years.(ABSTRACT TRUNCATED AT 250 WORDS)
1958年至1987年3月,我们共矫正了704例漏斗胸患者。该病在男孩(544例)中比女孩(160例)更常见。在大多数患者(86%)中,缺陷在出生时或出生后第一年内就很明显。133例患者被发现有肌肉骨骼异常(脊柱侧弯107例;脊柱后凸4例;肌病3例;波兰综合征3例;马凡综合征2例;皮埃尔·罗宾综合征2例;梨状腹综合征2例;神经纤维瘤病3例;脑瘫4例;结节性硬化症1例;先天性膈疝2例)。16例患者伴有先天性心脏病。37%的病例有胸壁畸形家族史,11%有脊柱侧弯病史。手术矫正采用统一技术,即双侧软骨膜下切除变形的肋软骨,并进行胸骨截骨术,切除前皮质楔形骨块并使后皮质骨折。用丝线缝合关闭截骨缺损以维持胸骨向前移位。在28例早期病例中,用斯氏针进行髓内固定来固定胸骨。所有修复手术的并发症发生率都很低(4.4%;气胸11例;伤口感染5例;伤口血肿3例;伤口裂开5例;肺炎3例;血清肿1例;咯血1例;血心包1例)。6例并发症与斯氏针固定有关(咯血、血清肿、血心包、气胸3例)。17例患者(2.7%)出现严重复发,其中12例需要再次手术。其余687例患者获得了满意的长期效果,随访时间从2周至27年不等。平均随访时间为4.3年。(摘要截选至250词)