Department of ENT, Addenbrooke's Hospital, Cambridge University Hospitals NHS Foundation Trust, Cambridge, United Kingdom.
Department of Radiology, Addenbrooke's Hospital, Cambridge University Hospitals NHS Foundation Trust, Cambridge, United Kingdom.
J Int Adv Otol. 2020 Aug;16(2):278-281. doi: 10.5152/iao.2020.7203.
Parachordoma is a rare soft tissue mixed tumor, associated with soft tissue myoepithelioma. It is typically growing slowly and considered less aggressive than other similar soft tissue tumors. However, it does recur sporadically, and on rare occasions, it has demonstrated the ability to metastasize. Although imaging is important, definitive diagnosis is achieved by histology, and it is typically treated by a wide local excision. We present the first reported case of a skull base parachordoma in a 15-year-old boy, managed with a wide local excision and with no signs of recurrence or metastases after 24 months of follow-up.
骨外孤立性中胚层瘤是一种罕见的软组织混合性肿瘤，与软组织肌上皮瘤相关。它的生长通常较为缓慢，被认为比其他类似的软组织肿瘤侵袭性更小。然而，它确实会偶尔复发，并且在极少数情况下，它已经表现出转移的能力。虽然影像学检查很重要，但明确的诊断是通过组织学来实现的，它通常通过广泛的局部切除来治疗。我们报告了首例 15 岁男孩颅底骨外孤立性中胚层瘤病例，采用广泛的局部切除，24 个月的随访中未见复发或转移迹象。
