Department of Pneumology and Allergy, Medical University of Lodz, Lodz, Poland.
Department of Radiology, National Tuberculosis and Lung Diseases Research Institute in Warsaw, Poland.
Adv Respir Med. 2020;88(1):41-93. doi: 10.5603/ARM.2020.0081.
This document presents the guidelines of the Polish Respiratory Society (PTChP, Polskie Towarzystwo Chorób Płuc) for diagnosis and treatment of idiopathic pulmonary fibrosis (IPF), developed by agroup of Polish experts.
The recommendations were developed in the form of answers to previously formulated questions concer-ning everyday diagnostic and therapeutic challenges. They were developed based on acurrent literature review using the Grading of Recommendations Assessment, Development and Evaluation (GRADE) methodology.
We formulated 28 recommendations for diagnosis (8), pharmacological treatment (12) as well as non-pharma-cological and palliative therapy (8). The experts suggest that surgical lung biopsy (SLB) not be performed in patients with the probable usual interstitial pneumonia (UIP) pattern, with an appropriate clinical context and unanimous opinion of a multidisciplinary team. The experts recommend using antifibrotic agents in IPF patients and suggest their use irrespective of the degree of functional impairment. As regards non-pharmacological and palliative treatment, strong re-commendations were formulated regarding pulmonary rehabilitation, oxygen therapy (in patients with chronic respiratory failure), preventive vaccinations as well as referring IPF patients to transplant centres. Table 1 presents an aggregate list of recommendations.
The Polish Respiratory Society Working Group developed guidelines for IPF diagnosis and treatment.
本文介绍了波兰呼吸学会（PTChP，Polskie Towarzystwo Chorób Płuc）制定的特发性肺纤维化（IPF）诊断和治疗指南，由一组波兰专家编写。
本指南以回答日常诊断和治疗挑战相关问题的形式呈现，采用当前文献综述，并使用推荐评估、制定与评价分级（GRADE）方法。
我们制定了 28 条诊断（8 条）、药物治疗（12 条）以及非药物和姑息治疗（8 条）建议。专家建议，对于可能为普通型间质性肺炎（UIP）模式、具有适当临床背景且多学科团队意见一致的患者，不进行外科肺活检（SLB）。专家建议在 IPF 患者中使用抗纤维化药物，并建议无论功能损害程度如何都应使用。关于非药物和姑息治疗，强烈建议进行肺康复、氧疗（慢性呼吸衰竭患者）、预防接种，并将 IPF 患者转至移植中心。表 1 列出了汇总的建议清单。
波兰呼吸学会工作组制定了 IPF 诊断和治疗指南。
