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一名年轻女性中罕见的多形性腺瘤恶变肌上皮癌

A Rare De Novo Myoepithelial Carcinoma Ex Pleomorphic Adenoma in a Young Woman.

作者信息

Ahuja Geeta, Taghipour Delaram J, Olufajo Olubode A, Davis Bonnie C, Shokrani Babak, Bond William R

机构信息

Clive O. Callender Howard-Harvard Clinical Sciences Outcomes Research Center, Department of Surgery, Howard University College of Medicine, Washington, DC, USA.

Johns Hopkins Bloomberg School of Public Health and Carey Business School, Baltimore, MD, USA.

出版信息

Case Rep Otolaryngol. 2020 Feb 26;2020:8325374. doi: 10.1155/2020/8325374. eCollection 2020.

Abstract

Carcinoma ex pleomorphic adenoma, an uncommon neoplasm of the parotid gland, accounts for less than 4% of salivary gland tumors. It arises from a benign pleomorphic adenoma presenting in the sixth to eighth decades of life. We present this as a unique account of a primary parotid gland carcinoma, arising from myoepithelial cells, without a known precursor lesion, in a 28-year-old woman. This presentation seeks to provide familiarity of an unusual presentation of an unexpected rare pathology in a young female patient and the tools utilized for an accurate diagnosis.

摘要

多形性腺瘤癌变是一种罕见的腮腺肿瘤,占涎腺肿瘤的比例不到4%。它起源于60至80岁出现的良性多形性腺瘤。我们在此报告一例独特的原发性腮腺癌病例,该病例发生在一名28岁女性身上,肿瘤由肌上皮细胞起源,无前驱病变。本报告旨在让大家熟悉年轻女性患者中这种意外罕见病理的不寻常表现,以及用于准确诊断的工具。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4a25/7061126/a9b0186b0aeb/CRIOT2020-8325374.001.jpg

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