Carretta Angelo, Ciriaco Paola, Bandiera Alessandro, Muriana Piergiorgio, Arrigoni Gianluigi, Negri Giampiero
Department of Thoracic Surgery, San Raffaele Hospital, Vita Salute San Raffaele University, Milan.
Monaldi Arch Chest Dis. 2020 Mar 12;90(1). doi: 10.4081/monaldi.2020.1223.
Primary chondrosarcoma of the trachea is an extremely rare tumor. We report two cases of tracheal chondrosarcoma describing the role of surgical and conservative treatment. Endoscopic treatment with rigid bronchoscopy was performed in both patients to restore airway patency and obtain histological specimens for diagnosis. One of the patients subsequently underwent successful tracheal resection and reconstruction. The other patient, who had a contraindication to surgical treatment due to associated diseases underwent iterative endoscopic LASER treatment and is alive three years after the first diagnosis. Surgical treatment remains the treatment of choice of tracheal chondrosarcoma. When surgery is contraindicated endoscopic treatment may allow relatively longterm survival due to the slow growth of these tumors.
气管原发性软骨肉瘤是一种极其罕见的肿瘤。我们报告两例气管软骨肉瘤病例,阐述手术和保守治疗的作用。两名患者均接受了硬质支气管镜下的内镜治疗,以恢复气道通畅并获取组织学标本用于诊断。其中一名患者随后成功接受了气管切除和重建手术。另一名患者因合并疾病存在手术治疗禁忌证,接受了反复的内镜激光治疗,自首次诊断后已存活三年。手术治疗仍然是气管软骨肉瘤的首选治疗方法。当手术禁忌时,由于这些肿瘤生长缓慢,内镜治疗可能会带来相对长期的生存。