Tucciarone Manuel, Heredia-Llinas Carlos, Lowy-Benoliel Alejandro, Souviron-Encabo Rosalia, Martínez-Guirado Tomas, Álvarez-Morujo Ricardo González-Orus
Department of Otorhinolaryngology, Gregorio Marañón Hospital, Madrid, SPAIN.
Iran J Otorhinolaryngol. 2020 Mar;32(109):109-112. doi: 10.22038/ijorl.2019.39741.2310.
Thyroid gland fibrosarcomas are extremely rare tumors, and only very few cases have been described in the literature. There are no set recommendations along with follow-ups regarding the treatment of these tumors. Moreover, the prognosis is poor with a very short life expectancy.
We present an 81-year-old patient who was suffering from increasing dysphagia and dysphonia related to a painless giant cervical mass, which presented with progressive growth for the preceding months. After a core needle biopsy with a suspicion of a solitary fibrous tumor, total excision of the tumor was successfully performed, and the pathology examination revealed a fibrosarcoma. Following surgery, radiotherapy was decided in the oncological multidisciplinary meeting; however, the patient refused it. There were neither new clinical symptoms nor tumor recurrence after an 18-month follow-up.
Although it is a very rare tumor, primary fibrosarcoma of the thyroid gland should be kept in mind in the differential diagnosis of neck tumors.
甲状腺纤维肉瘤是极其罕见的肿瘤，文献中仅描述了极少数病例。对于这些肿瘤的治疗，没有既定的建议以及随访方案。此外，预后很差，预期寿命很短。
我们报告一例81岁患者，因无痛性巨大颈部肿块出现吞咽困难和发音困难加重，该肿块在之前几个月呈进行性生长。在怀疑为孤立性纤维瘤进行粗针活检后，成功进行了肿瘤全切，病理检查显示为纤维肉瘤。手术后，在肿瘤多学科会议上决定进行放疗；然而，患者拒绝了。18个月的随访后既没有新的临床症状，也没有肿瘤复发。
尽管是非常罕见的肿瘤，但在颈部肿瘤的鉴别诊断中应考虑到原发性甲状腺纤维肉瘤。
