Gynecology Department, The First Affiliated Hospital, College of Medicine, Zhejiang University, Hangzhou, China.
J Int Med Res. 2020 Mar;48(3):300060520905438. doi: 10.1177/0300060520905438.
Rhabdomyosarcoma (RMS) is a common soft tissue tumor in children, but it is rare in adults. Alveolar rhabdomyosarcoma (ARMS) is a subtype of RMS and is extremely rare in adults, especially concerning the genital tract. We report a case of a 20-year-old woman who was admitted to and treated in our hospital for an RMS of the vulva. The patient presented with local recurrence and bone metastasis during chemotherapy after surgery and died within 1 year of diagnosis. Based on a literature review, the prognosis of ARMS in adults is poor. The treatment strategy for ARMS is not well established yet. The lungs and bone are two common sites of metastasis of ARMS.
横纹肌肉瘤(RMS)是儿童常见的软组织肿瘤,但在成人中很少见。腺泡状横纹肌肉瘤(ARMS)是 RMS 的一种亚型,在成人中极为罕见,特别是在生殖道。我们报告了一例 20 岁女性,因外阴 RMS 在我院住院治疗。该患者在手术后化疗期间出现局部复发和骨转移,并在诊断后 1 年内死亡。基于文献回顾,成人 ARMS 的预后较差。ARMS 的治疗策略尚未确定。肺和骨是 ARMS 常见的转移部位。