Paediatric and Adolescent Gynaecology, Department of Paediatric Surgery, Queensland Children's Hospital, South Brisbane, Queensland, Australia
School of Medicine, The University of Queensland, St Lucia, Queensland, Australia.
BMJ Case Rep. 2020 Apr 9;13(4):e231749. doi: 10.1136/bcr-2019-231749.
HAIR-AN-a syndrome of hyperandrogenism (HA), insulin resistance (IR) and acanthosis nigricans (AN)-is a specific subphenotype of polycystic ovary syndrome (PCOS), and it is seen in almost 5% of all women with hyperandrogenism. An adolescent girl aged 11 years old was referred with adrenarche, hyperandrogenism and obesity commencing at age 8. Clinical and biochemical investigations confirmed significant hyperandrogenism and insulin resistance, and a diagnosis of HAIR-AN syndrome was made after exclusion of other differential diagnoses. HAIR-AN syndrome is an important diagnosis for the adolescent gynaecologist to be aware of, and it requires a multidisciplinary approach, including endocrinology input, for optimal management. Weight loss, lifestyle modification and combined hormonal pill and metformin are considered first-line treatment.
多毛-黑棘皮-胰岛素抵抗综合征(HAIR-AN 综合征)是多囊卵巢综合征(PCOS)的一种特殊亚表型,几乎见于所有高雄激素血症女性的 5%。一名 11 岁的青春期女孩因 8 岁时开始出现肾上腺早现、高雄激素血症和肥胖而被转介。临床和生化检查证实存在明显的高雄激素血症和胰岛素抵抗,在排除其他鉴别诊断后,诊断为 HAIR-AN 综合征。HAIR-AN 综合征是青春期妇科医生需要注意的一个重要诊断,需要内分泌科的多学科参与,以实现最佳管理。减肥、生活方式改变以及联合激素避孕药和二甲双胍被认为是一线治疗方法。