Department of Medicine and Clinical Science, Graduate School of Medical Sciences, Kyushu University, 3-1-1 Maidashi, Higashi-Ku, Fukuoka, 8128582, Japan.
CEN Case Rep. 2020 Aug;9(3):278-284. doi: 10.1007/s13730-020-00473-x. Epub 2020 Apr 10.
A 71-year-old woman was hospitalized for the treatment of fatigue, fever, and cough. On admission, she showed increased serum inflammation markers, severe anemia, pulmonary hemorrhage, and advanced acute kidney injury requiring hemodialysis. Her serum anti-glomerular basement membrane (GBM) antibody titer was found to be extremely high on the 7th hospital day. She was eventually diagnosed with anti-GBM disease. She was treated with a combination of corticosteroid pulse therapy, oral prednisolone and cyclophosphamide, and plasma exchange, but continued to require maintenance hemodialysis for end-stage kidney disease. During her treatment, she suddenly developed headache, blindness, seizure, and consciousness disturbance. She was diagnosed by magnetic resonance imaging with posterior reversible encephalopathy syndrome (PRES) with subcortical cerebral hemorrhage. Both the PRES and cerebral hemorrhage subsided soon after control of her hypertension and reinforcement of immunosuppressive treatment. PRES, particularly when accompanied by cerebral hemorrhage, may cause irreversible and lethal neurological abnormalities, and nephrologists should, therefore, be aware of the potential risk of PRES in patients with anti-GBM disease. We discuss the current case in the light of the previous literature.
一位 71 岁女性因疲劳、发热和咳嗽住院治疗。入院时,她表现出炎症标志物升高、严重贫血、肺出血和晚期急性肾损伤,需要血液透析。第 7 天,她的血清抗肾小球基底膜 (GBM) 抗体滴度极高。最终被诊断为抗 GBM 疾病。她接受了皮质类固醇脉冲治疗、口服泼尼松龙和环磷酰胺以及血浆置换的联合治疗,但由于终末期肾病仍继续需要维持性血液透析。在治疗过程中,她突然出现头痛、失明、癫痫和意识障碍。磁共振成像诊断为后可逆性脑病综合征 (PRES) 伴皮质下脑内出血。高血压控制和免疫抑制治疗加强后,PRES 和脑出血很快消退。PRES,特别是伴有脑出血时,可能导致不可逆和致命的神经功能异常,因此,肾科医生应意识到抗 GBM 疾病患者发生 PRES 的潜在风险。我们根据以往文献对当前病例进行了讨论。