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色素性静脉旁视网膜脉络膜萎缩:一种疾病实体?

Pigmented paravenous retinochoroidal atrophy: a nosologic entity?

作者信息

Klop K, van Schooneveld M J

机构信息

The Netherlands Ophthalmic Research Institute, Department of Ophthalmogenetics, Amsterdam.

出版信息

Doc Ophthalmol. 1988 Oct-Nov;70(2-3):185-93. doi: 10.1007/BF00154452.

DOI:10.1007/BF00154452
PMID:3234183
Abstract

A new case of pigmented paravenous retinochoroidal atrophy is described. Besides the characteristic fundus picture, this 21-year-old male showed a remarkable difference in retinal function between the two eyes, the function of the left eye being much more impaired. This might suggest a progressive condition, in which the right eye lags behind. In addition this patient had a vitreoretinal degeneration resulting in five peripheral retinal tears in the right eye.

摘要

本文描述了一例色素性静脉旁视网膜脉络膜萎缩的新病例。除了典型的眼底图像外,这位21岁男性的双眼视网膜功能存在显著差异,左眼功能受损更为严重。这可能提示病情呈进行性发展,右眼随后也会受到影响。此外,该患者还患有玻璃体视网膜变性,导致右眼周边视网膜出现5处裂孔。

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Pigmented paravenous retinochoroidal atrophy: a nosologic entity?色素性静脉旁视网膜脉络膜萎缩:一种疾病实体?
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引用本文的文献

1
A familial case of pigmented paravenous retinochoroidal atrophy with asymmetrical fundus manifestations.一例具有不对称眼底表现的色素性静脉旁视网膜脉络膜萎缩家族性病例。
Graefes Arch Clin Exp Ophthalmol. 2006 Jul;244(7):874-7. doi: 10.1007/s00417-005-0179-0. Epub 2005 Nov 29.

本文引用的文献

1
RETINO-CHOROIDITIS RADIATA.放射性视网膜脉络膜炎
Br J Ophthalmol. 1937 Dec;21(12):645-8. doi: 10.1136/bjo.21.12.645.
2
Pigmented paravenous chorioretinal atrophy.色素性静脉旁脉络膜视网膜萎缩
Am J Ophthalmol. 1983 Sep;96(3):338-44. doi: 10.1016/s0002-9394(14)77825-0.
3
[Pigmented paravenous chorioretinal degeneration].色素性静脉旁脉络膜视网膜变性
Bull Soc Ophtalmol Fr. 1968 Jul-Aug;68(7):681-4.
4
[Pigmented, paravenous retinal and chorioidal atrophy].[色素沉着性、静脉旁视网膜及脉络膜萎缩]
Klin Monbl Augenheilkd. 1968;153(6):770-5.
5
[Unilateral pigmented paravenous chorio-retinal degeneration].[单侧色素性静脉旁脉络膜视网膜变性]
Ann Ottalmol Clin Ocul. 1967 Dec;93(12):1294-8.
6
Pigmented paravenous retino-choroidal atrophy. Helicoid retino-choriodal atrophy.色素性静脉旁视网膜脉络膜萎缩。螺旋状视网膜脉络膜萎缩。
Br J Ophthalmol. 1973 Aug;57(8):584-7. doi: 10.1136/bjo.57.8.584.
7
ERG and EOG in progressive paravenous retinochoroidal atrophy.进行性静脉旁视网膜脉络膜萎缩的视网膜电图和眼电图
Doc Ophthalmol. 1986 Jan 31;62(1):25-9. doi: 10.1007/BF00140543.
8
Pigmented paravenous retinochoroidal atrophy (PPRA).色素性静脉旁视网膜脉络膜萎缩(PPRA)。
Doc Ophthalmol. 1986 Sep 30;63(3):209-37. doi: 10.1007/BF00160758.
9
Hereditary pigmented paravenous chorioretinal atrophy.遗传性色素性静脉旁脉络膜视网膜萎缩
Arch Ophthalmol. 1986 Nov;104(11):1636-40. doi: 10.1001/archopht.1986.01050230074036.
10
Pigmented paravenous retinochorodial atrophy.色素性静脉旁视网膜脉络膜萎缩
Am J Ophthalmol. 1975 Oct;80(4):630-5. doi: 10.1016/0002-9394(75)90393-1.