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色素性静脉旁视网膜脉络膜萎缩

Pigmented paravenous retinochorodial atrophy.

作者信息

Pearlman J T, Kamin D F, Kopelow S M, Saxton J

出版信息

Am J Ophthalmol. 1975 Oct;80(4):630-5. doi: 10.1016/0002-9394(75)90393-1.

DOI:10.1016/0002-9394(75)90393-1
PMID:1180304
Abstract

Three male patients had paravenous pigmented retinochoroidal atrophy. Extensive retinal function tests showed characteristic retinal pigment epithelial abnormalities on fluorescein angiography, loss of peripheral visual field, diminution of the electroretinographic b-wave, and elevated rod threshold on dark adaptometry. The disease appears to be more progressive than previously indicated, and in late stages, may cause legal blindness through involvement of the posterior pole. No treatment is known.

摘要

三名男性患者患有静脉旁色素性视网膜脉络膜萎缩。广泛的视网膜功能测试显示,荧光素血管造影有特征性视网膜色素上皮异常、周边视野丧失、视网膜电图b波降低以及暗适应测量中视杆阈值升高。该疾病似乎比之前指出的更具进展性,在晚期,可能通过累及后极导致法定失明。目前尚无已知的治疗方法。

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Pigmented paravenous retinochorodial atrophy.色素性静脉旁视网膜脉络膜萎缩
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Pigmented paravenous retinochoroidal atrophy.色素性静脉旁视网膜脉络膜萎缩
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Pigmented paravenous retinochoroidal atrophy.色素性静脉旁视网膜脉络膜萎缩
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引用本文的文献

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Pigmented paravenous chorioretinal atrophy: Updated scenario.色素性静脉旁脉络膜视网膜萎缩:最新情况
Eur J Ophthalmol. 2024 Jul;34(4):941-951. doi: 10.1177/11206721231199118. Epub 2023 Sep 5.
2
Multimodal image characterization of paravenous atrophy.静脉旁萎缩的多模态图像特征
GMS Ophthalmol Cases. 2019 Jul 16;9:Doc27. doi: 10.3205/oc000116. eCollection 2019.
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Pigmented paravenous retinochoroidal atrophy (Review).色素性静脉旁视网膜脉络膜萎缩(综述)
Exp Ther Med. 2014 Jun;7(6):1439-1445. doi: 10.3892/etm.2014.1648. Epub 2014 Mar 28.
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Pigmented paravenous chorioretinal atrophy with Coat's like response.色素性脉络膜视网膜旁萎缩伴 Coat 样反应。
Indian J Ophthalmol. 2013 Oct;61(10):586-8. doi: 10.4103/0301-4738.121083.
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Preserved para-arteriole retinal pigment epithelium (PPRPE) in retinitis pigmentosa.色素性视网膜炎中的保存的视网膜小动脉旁视网膜色素上皮(PPRPE)
Br J Ophthalmol. 1982 Jan;66(1):26-30. doi: 10.1136/bjo.66.1.26.
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ERG and EOG in progressive paravenous retinochoroidal atrophy.进行性静脉旁视网膜脉络膜萎缩的视网膜电图和眼电图
Doc Ophthalmol. 1986 Jan 31;62(1):25-9. doi: 10.1007/BF00140543.
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Autoimmunity in hereditary retinal degeneration. I. Basic studies.遗传性视网膜变性中的自身免疫。I. 基础研究。
Br J Ophthalmol. 1985 Jan;69(1):19-24. doi: 10.1136/bjo.69.1.19.
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Pigmented paravenous retinochoroidal atrophy (PPRA).色素性静脉旁视网膜脉络膜萎缩(PPRA)。
Doc Ophthalmol. 1986 Sep 30;63(3):209-37. doi: 10.1007/BF00160758.
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Retinal microangiopathy in pigmented paravenous chorioretinal atrophy.色素性静脉旁脉络膜视网膜萎缩中的视网膜微血管病变。
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