Naqvi Syed Haseeb Raza, Ahmed Ishfaq, Ali Pir Sheeraz, Alam Maqsood, Zab Jehan, Naung Tun Han
National Institute of Cardiovascular Diseases, Karachi, Sindh, Pakistan.
Department of Adult Cardiology, Chaudhry PervaizElahi Institute of cardiology Multan, Punjab, Pakistan.
Eur J Case Rep Intern Med. 2020 Mar 24;7(5):001484. doi: 10.12890/2020_001484. eCollection 2020.
Persistent left superior vena cava (PLSVC) is the most common variation of anomalous venous return to the heart and present in 0.1-0.5% of the general population. The left anterior cardinal veins typically obliterate during early cardiac development but failure of involution results in PLSVC. It is an asymptomatic congenital anomaly, usually discovered while performing interventions through the left subclavian vein or during cardiovascular imaging. PLSVC can be associated with cardiac arrhythmias and congenital heart disease. We present two cases of PLSVC: first, a 68-year-old male who presented with complete heart block, for which a temporary pacemaker was initially inserted followed by a permanent pacemaker; second, a 53-year-old female with a history of hypertension and ischemic cardiomyopathy with a left ventricular ejection fraction of 25%, and a survivor of sudden cardiac death, who underwent an implantable cardioverter-defibrillator (ICD) for secondary prevention. Both cases of PLSVC were detected incidentally during the transvenous approach to the heart. PLSVC was suspected by the unusually left medial position of the lead, while cineflouroscopy showed the venous trajectory toward the coronary sinus and drainage into the right atrium. It is technically difficult to cross the wire through the tricuspid valve when coming from the PLSVC and coronary sinus without making a loop in the right atrium, which is known as a wide loop technique. PLSVC is an uncommon anomalous anatomical variant and should be recognized appropriately by specialists who frequently carry out procedures through the left subclavian vein, such as implantation of permanent pacemaker, ICD and cardiac resynchronization therapy. It should also be recognized that wide loop formation of the right ventricular lead in the right atrium is helpful to cross the tricuspid valve and to affix the lead in the right ventricle.
Persistent left superior vena cava is an anatomical variant that should be recognized by specialists who frequently carry procedures through the left subclavian vein (e.g. implantation of a permanent pacemaker, implantable cardioverter-defibrillator and cardiac resynchronization therapy).Maneuvers like wide loop formation of the right ventricular lead in the right atrium is helpful to cross the tricuspid valve and to affix the lead in the right ventricle.The cardiac imaging specialist should also suspect and rule out PLSVC on encountering a dilated coronary sinus on any imaging modality.
永存左上腔静脉(PLSVC)是心脏异常静脉回流最常见的变异情况,在普通人群中的发生率为0.1% - 0.5%。左前主静脉通常在心脏早期发育过程中闭塞,但退化失败会导致PLSVC。它是一种无症状的先天性异常,通常在通过左锁骨下静脉进行干预操作或心血管成像时被发现。PLSVC可能与心律失常和先天性心脏病有关。我们报告两例PLSVC病例:第一例,一名68岁男性,表现为完全性心脏传导阻滞,最初植入临时起搏器,随后植入永久起搏器;第二例,一名53岁女性,有高血压和缺血性心肌病病史,左心室射血分数为25%,是心脏性猝死幸存者,接受植入式心律转复除颤器(ICD)进行二级预防。两例PLSVC均在经静脉途径进入心脏的过程中偶然被发现。由于导线异常位于左侧内侧位置而怀疑有PLSVC,而电影荧光透视显示静脉走向冠状窦并引流至右心房。当从PLSVC和冠状窦进入时,在不使导线在右心房形成环(即宽环技术)的情况下,将导线穿过三尖瓣在技术上是困难的。PLSVC是一种罕见的异常解剖变异,经常通过左锁骨下静脉进行操作的专科医生,如进行永久起搏器植入、ICD植入和心脏再同步治疗的医生,应适当认识到这一点。还应认识到,在右心房中形成右心室导线的宽环有助于穿过三尖瓣并将导线固定在右心室。
永存左上腔静脉是一种解剖变异,经常通过左锁骨下静脉进行操作的专科医生(如永久起搏器植入、植入式心律转复除颤器植入和心脏再同步治疗)应认识到这一点。在右心房中形成右心室导线的宽环等操作有助于穿过三尖瓣并将导线固定在右心室。心脏影像专科医生在任何成像方式下遇到扩张的冠状窦时,也应怀疑并排除PLSVC。