Department of Anesthesia and Peri-operative Medicine, Manchester University Hospital NHS Foundation Trust, University of Manchester, Manchester, United Kingdom.
Department of Anesthesia, Royal Oldham Hospital, Manchester, United Kingdom.
Korean J Anesthesiol. 2021 Aug;74(4):342-349. doi: 10.4097/kja.20181. Epub 2020 May 20.
Shone's syndrome is a rare complex congenital cardiac condition, characterized by a supra-valvular mitral ring, parachute deformity of the mitral valve, aortic stenosis, and coarctation of the aorta.
A 26-year-old parturient with partial Shone's syndrome presented to our delivery unit in pulmonary edema. She underwent a scheduled cesarean section performed under a combined spinal-epidural anesthetic at 33 weeks. She had multidisciplinary input from the cardiac, obstetric, and anesthetic teams, which led to a good outcome. A review of the five published case reports of Shone's syndrome in pregnancy is presented along with key findings.
Our case report and the review highlight the successful use of combined spinal-epidural anesthetic and provides guidance to the multidisciplinary team on the varied presentation and the optimum management of women with Shone's syndrome during the peripartum period.
Shone 综合征是一种罕见的复杂先天性心脏疾病，其特征为瓣上二尖瓣环、二尖瓣降落伞样畸形、主动脉瓣狭窄和主动脉缩窄。
一位 26 岁的产妇因肺水肿被收入我院分娩单元，她在孕 33 周时接受了椎管内麻醉联合全身麻醉下的择期剖宫产术。心脏科、产科和麻醉科的多学科团队为其提供了支持，最终母婴结局良好。本文报告了 5 例妊娠合并 Shone 综合征的病例，并对其关键发现进行了回顾。
我们的病例报告和综述强调了椎管内麻醉联合全身麻醉的成功应用，并为多学科团队提供了指导，以帮助他们了解不同表现形式，并在围产期为 Shone 综合征产妇提供最佳管理。
