Ramponi Sara, Gnetti Letizia, Marvisi Maurizio, Bertorelli Giuseppina, Chetta Alfredo
Dept. of Internal Medicine, Istituto Figlie di San Camillo, Cremona.
Pathology Unit, University Hospital of Parma, Parma, Italy.
Sarcoidosis Vasc Diffuse Lung Dis. 2018;35(1):74-80. doi: 10.36141/svdld.v35i1.6161. Epub 2018 Apr 28.
Immunoglobulin (Ig) G4-related disease (IgG4-RD) is a recently described systemic inflammatory disease associated with elevated circulating levels of IgG4. IgG4-RD may affect one or more organs and lesions can present synchronously or metachronously in different organs. Pulmonary involvement of IgG4-related disease includes airway, lung parenchyma, pleura and mediastinum. In this article, we report two cases of IgG4-RD to show the multifaceted manifestations of this disease in the lungs. .
免疫球蛋白(Ig)G4相关疾病(IgG4-RD)是一种最近被描述的全身性炎症性疾病,与循环中IgG4水平升高有关。IgG4-RD可累及一个或多个器官,病变可在不同器官同时或先后出现。IgG4相关疾病的肺部受累包括气道、肺实质、胸膜和纵隔。在本文中,我们报告了两例IgG4-RD病例,以展示该疾病在肺部的多方面表现。