胰腺实性假乳头状瘤：儿童中的一种罕见实体瘤。

Solid pseudopapillary tumor of the pancreas: a rare entity in children.

作者信息

Berrada Ghita, Belaaroussi Soukaina, Chbani Kamilia, Salam Siham, Laoudiyi Dalal, Ouzidane Lahcen, Kebir Asmaa El, Guebessi Nisrine Bennani, Benayad Samira, Mernissi Farida, Karkouri Mehdi, Anis Salma, Zemmouri Mounia Al

机构信息

Department of Pediatric Radiology, Abderrahim Harouchi Pediatric Hospital, Ibn Rochd University Hospital, Casablanca, Morocco.

Department of Pathology, Ibn Rochd University Hospital, Casablanca, Morocco.

出版信息

Pan Afr Med J. 2020 Apr 27;35:137. doi: 10.11604/pamj.2020.35.137.22404. eCollection 2020.

DOI:10.11604/pamj.2020.35.137.22404

PMID:32655751

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7335250/

Abstract

Solid pseudopapillary tumors (SPTs) constitute 0.2 to 2.7% of non-endocrine primary tumors of the pancreas and comprise the majority (70%) of pediatric pancreatic neoplasms. These tumors are of unclear pathogenesis, low malignancy and favorable prognosis. Surgical resection offers an excellent chance for longterm survival, even in the presence of distant metastasis. The objective of this study is to review our experience in the management of SPT in a 12 years old girl at the pediatric hospital of the University hospital of Casablanca, in Morocco and provide an update on current management in pediatric population.

摘要

实性假乳头状肿瘤（SPTs）占胰腺非内分泌原发性肿瘤的0.2%至2.7%，且构成儿童胰腺肿瘤的大多数（70%）。这些肿瘤的发病机制尚不清楚，恶性程度低，预后良好。即使存在远处转移，手术切除也为长期生存提供了绝佳机会。本研究的目的是回顾我们在摩洛哥卡萨布兰卡大学医院儿科对一名12岁女孩的实性假乳头状肿瘤的治疗经验，并提供儿科人群当前治疗方法的最新情况。