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亚急性硬化性全脑炎:成人急性皮质视觉障碍的罕见病因。

Subacute sclerosing panencephalitis: a rare cause of acute cortical visual impairment in an adult.

作者信息

Herath Hmmtb, Nandasiri Shanika, Chandrakumara Amila, Jayamaha Jude, Senanayake Sunethra, Goonaratne Kishara

机构信息

Senior registrar in neurology, 294945National Hospital of Sri Lanka, Colombo, Sri Lanka.

Senior Registrar in neuroradiology, Department of Neuroradiology, 294945National Hospital of Sri Lanka, Colombo, Sri Lanka.

出版信息

Trop Doct. 2020 Oct;50(4):354-358. doi: 10.1177/0049475520939325. Epub 2020 Jul 14.

DOI:10.1177/0049475520939325
PMID:32664798
Abstract

Adult onset subacute sclerosing panencephalitis (SSPE) after the third decade of life is rare and the manifestations can mimic disorders such as dysmyelinating and metabolic disorders. This case report presents a patient with acute binocular visual impairment in his fifth decade as the first manifestation of SSPE. This is preventable with immunisation against measles. A prior history of measles infection may not be forthcoming in adult onset SSPE. This should be kept in mind as a differential diagnosis when a patient from endemic area presents with acute visual loss even in the absence of classic features. Periodic generalised discharges on the EEG without myoclonus may be seen in this condition rarely as in this case.

摘要

成年期发病的亚急性硬化性全脑炎(SSPE)在30岁以后较为罕见,其表现可能类似于脱髓鞘疾病和代谢性疾病等病症。本病例报告介绍了一名50岁患者,以急性双眼视力障碍作为SSPE的首发表现。通过麻疹免疫可预防此病。成年期发病的SSPE患者可能没有麻疹感染病史。当来自流行地区的患者出现急性视力丧失时,即使没有典型特征,也应将此病作为鉴别诊断考虑在内。在这种情况下,脑电图上可能很少出现周期性广泛性放电而无肌阵挛,就像本病例一样。

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