Sung K B, Chang D I, Kim J H, Kim M H, Hahm C K, Jeon S C
Department of Neurology, College of Medicine, Hanyang University, Seoul, Korea.
J Korean Med Sci. 1987 Jun;2(2):117-21. doi: 10.3346/jkms.1987.2.2.117.
Aneurysm of the vein of Galen is a very rare disease. The authors present a case of secondary aneurysm of the vein of Galen which was confirmed by characteristic clinical symptoms, brain CT and angiographic findings. The patient was a 14-year-old right handed girl with intermittent headache, nausea, vomiting, dysphasia and gait disturbance. Neurologic examination revealed dysarthria, nasal voice, blurring of both margins of optic discs, truncal ataxia and dysdiadochokinesia. Sensory function was normal but right hemiparesis was seen. Roentgenogram of the skull revealed diffuse thinning of the calvarium, widening of sella turcica and erosion of clinoid processes. Computed tomogram of the brain showed dilatation of all ventricles and round hyperdense mass behind the third ventricle in the midline. The lesion was enhanced markedly and homogeneously. Left and right internal carotid angiograms showed arteriovenousmal-formation with drainage to the aneurysm of the vein of Galen.
大脑大静脉动脉瘤是一种非常罕见的疾病。作者报告了一例大脑大静脉继发性动脉瘤病例，该病例经特征性临床症状、脑部CT及血管造影结果得以确诊。患者为一名14岁右利手女孩，有间歇性头痛、恶心、呕吐、言语困难及步态障碍。神经系统检查发现构音障碍、鼻音、双侧视盘边缘模糊、躯干性共济失调及轮替运动障碍。感觉功能正常，但存在右侧偏瘫。头颅X线片显示颅骨弥漫性变薄、蝶鞍增宽及床突侵蚀。脑部计算机断层扫描显示所有脑室扩张，中线第三脑室后方有圆形高密度肿块。该病变有明显且均匀的强化。左右颈内动脉血管造影显示动静脉畸形并引流至大脑大静脉动脉瘤。
