Schorn Lara, Lommen Julian, Depprich Rita, Kübler Norbert, Rana Majeed, Heydt Carina, Lohneis Philipp, Kaiser Peter, Sproll Christoph
Department of Oral and Maxillofacial Surgery, Medical Faculty, Heinrich-Heine-University and University Hospital Düsseldorf, D-40225 Düsseldorf, Germany.
Department of Pathology, Medical Faculty, University Hospital Cologne, D-50937 Cologne, Germany.
Mol Clin Oncol. 2020 Oct;13(4):23. doi: 10.3892/mco.2020.2093. Epub 2020 Jul 16.
Tumors of the follicular dendritic cells (FDC-Sarcoma) represent a rare entity with only about 200 cases reported worldwide. The majority (60%) of cases arise primarily in cervical, abdominal or axillar lymph nodes, but extra nodal origin from secondary lymphatic tissue like the tonsils, Waldeyer's ring or MALT is also common (40%). The current report presents a characteristic course of a cervical FDC-Sarcoma, with its challenges in establishing the initial diagnosis and the struggle for therapeutic options. The FDC-Sarcoma presented recurrently for four times. Three different university hospitals in Germany were involved in the patients' treatment. Due to the patients' refusal, no adjuvant therapy was applied. In the end, a neck dissection was performed. The patient was closely followed up and has been recurrence-free for 10 years. This case suggests operative resection in combination with a neck dissection as a curative therapy for FDC-Sarcoma of the head and neck.
滤泡树突状细胞肿瘤(FDC肉瘤)是一种罕见疾病,全球仅报告约200例。大多数病例(60%)主要发生在颈部、腹部或腋窝淋巴结,但起源于扁桃体、Waldeyer环或MALT等二级淋巴组织的结外部位也很常见(40%)。本报告介绍了一例颈部FDC肉瘤的典型病程,包括其在确立初始诊断时面临的挑战以及治疗方案的抉择。该FDC肉瘤复发了四次。德国的三家不同大学医院参与了患者的治疗。由于患者拒绝,未进行辅助治疗。最后,进行了颈部清扫术。对患者进行了密切随访,患者已无复发存活10年。该病例提示手术切除联合颈部清扫术可作为头颈部FDC肉瘤的治愈性治疗方法。