Asaad Saywan K, Salih Kardo M, Kakamad Fahmi H, Salih Abdulwahid M, Mohammed Shvan H
Smart Health Tower, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq; Shar Hospital, Department of Orthopedic, Sulaimani, Kurdistan, Iraq; College of Medicine, University of Sulaimani, Sulaimani, Kurdistan, Iraq.
Shar Hospital, Department of Orthopedic, Sulaimani, Kurdistan, Iraq.
Int J Surg Case Rep. 2020;74:260-262. doi: 10.1016/j.ijscr.2020.07.078. Epub 2020 Aug 11.
Pigmented villonodular synovitis (PVNS) of the hip joint associated with developmental dysplasia of the hip joint (DDH) is an extremely rare co-presentation. The aim of this study is to report a case of PVNS associated with DDH.
A 26-year-old women, a known case of DDH, presented with progressive right hip pain for one month duration. She was able to perform all the right hip movements with limitation due to pain. Plain radiographs showed a hip dislocation. Through a posterior incision, a mass of brown fibro-fatty soft tissue emerged. The specimen was sent for histopathological examination, The findings were variable mixture of giant cells, hemosiderin, and brown pigmentation in the synoviocyte cytoplasm.
Although both conditions were previously described separately, the significance of co-incidence of DDH and PVNS is not well understood due to the rarity of the association.
Co-incidence of DDH with PVNS is an extremely rare finding but could be safely managed if caught early in the beginning of the disease.
髋关节色素沉着绒毛结节性滑膜炎（PVNS）合并髋关节发育不良（DDH）是一种极为罕见的共现情况。本研究的目的是报告一例PVNS合并DDH的病例。
一名26岁女性，已知患有DDH，出现右髋部进行性疼痛1个月。由于疼痛，她能够进行所有右髋部活动，但有一定限制。X线平片显示髋关节脱位。通过后入路切口，发现一团棕色纤维脂肪软组织。标本送去做组织病理学检查，结果显示滑膜细胞胞质内有巨细胞、含铁血黄素和棕色色素沉着的不同混合情况。
尽管这两种情况之前曾分别有过描述，但由于这种关联极为罕见，DDH与PVNS同时出现的意义尚未得到充分理解。
DDH与PVNS同时出现是一种极其罕见的情况，但如果在疾病早期发现，可得到安全的治疗。
