Ho Chi Long, Lam Jeremy Jh, Chen Robert Chun
Department of Radiology, Changi General Hospital, Singapore, Singapore.
BJR Case Rep. 2020 Sep 29;6(2):20190081. doi: 10.1259/bjrcr.20190081. eCollection 2020 Sep.
Primary intracranial tumours rarely metastasise outside of the central nervous system (CNS). This report describes a rare case of recurrent meningeal haemangiopericytoma with extensive systemic metastases, which eventually resulted in a fatal outcome. We discuss some prevailing theories as to the rarity of extracranial metastases from primary CNS haemangiopericytoma, and elucidate the epidemiology, imaging features, differential diagnosis, treatment, and prognosis of this unusual but surprisingly aggressive meningeal tumour. Besides aggressive treatment for local tumour control, patients with primary CNS haemangiopericytoma require long-term post-treatment surveillance to detect systemic metastases.
原发性颅内肿瘤很少转移至中枢神经系统（CNS）以外。本报告描述了一例罕见的复发性脑膜血管外皮细胞瘤伴广泛全身转移，最终导致致命结局的病例。我们讨论了一些关于原发性CNS血管外皮细胞瘤颅外转移罕见的主流理论，并阐明了这种不寻常但极具侵袭性的脑膜肿瘤的流行病学、影像学特征、鉴别诊断、治疗及预后。除了积极治疗以控制局部肿瘤外，原发性CNS血管外皮细胞瘤患者需要长期的治疗后监测以发现全身转移。
