Department of Human Pathology in Adult and Developmental Age 'Gaetano Barresi', University of Messina, Messina, Sicilia, Italy.
Department of Human Pathology in Adult and Developmental Age 'Gaetano Barresi', University of Messina, Messina, Sicilia, Italy
BMJ Case Rep. 2020 Nov 2;13(11):e236059. doi: 10.1136/bcr-2020-236059.
Acute haemorrhagic oedema of infancy (AHOI) is a rare condition and an unusual diagnosis for the paediatrician, as approximately 300 cases have been reported in literature so far. Although it was considered for years a less serious variant of Henoch-Schönlein purpura, nowadays it is thought to be a different entity, with his own characteristics and clinical outcome. In literature it is described as a benign condition, self-limiting and without any systemic involvement in most of the cases. We present an atypical case of AHOI with a severe presentation and which needed an aggressive and prolonged steroid therapy.
婴儿急性出血性水肿(AHOI)是一种罕见的疾病,也是儿科医生不常见的诊断,因为迄今为止,文献中大约报告了 300 例病例。虽然多年来它被认为是过敏性紫癜的一种较轻的变异型,但现在它被认为是一种不同的实体,具有自己的特征和临床结果。在文献中,它被描述为一种良性疾病,大多数情况下是自限性的,没有任何全身性受累。我们报告了一例非典型的 AHOI 病例,其表现严重,需要积极和长期的类固醇治疗。