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患有迅速进展性皮疹的婴儿。

Infant with a rapidly progressing rash.

机构信息

Department of Pediatrics, University at Buffalo Jacobs School of Medicine and Biomedical Sciences, Buffalo, NY, USA

Department of Pediatrics, University at Buffalo Jacobs School of Medicine and Biomedical Sciences, Buffalo, NY, USA.

出版信息

BMJ Case Rep. 2021 Jan 25;14(1):e239353. doi: 10.1136/bcr-2020-239353.

DOI:10.1136/bcr-2020-239353
PMID:33495190
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7839848/
Abstract

An infant presented to the emergency department with sudden onset of rapidly progressing erythematous macules and distal oedema. The rash was striking in appearance, covering most of the body, which raised concern for pressing infectious (eg, meningococcaemia) and other serious aetiologies. Nevertheless, the infant remained playful and was overall stable and posed a diagnostic and management dilemma. After an extensive workup and multispecialty consultations, the patient was eventually diagnosed with acute haemorrhagic oedema of infancy, a benign leucocytoclastic vasculitis. The patient received no treatment and resolution of the rash occurred within 7 days of onset. Recognition of this condition and its benign nature can spare patients from an extensive workup and reduce anxiety for both family members and healthcare providers.

摘要

一名婴儿因突然出现迅速进展的红斑性斑疹和远端水肿而到急诊就诊。皮疹外观引人注目,覆盖了大部分身体,这引起了对传染性疾病(例如脑膜炎球菌血症)和其他严重病因的关注。然而,婴儿仍然活泼,整体情况稳定,这构成了诊断和管理上的难题。经过广泛的检查和多专科会诊,该患者最终被诊断为婴儿急性出血性水肿,一种良性白细胞碎裂性血管炎。该患者未接受治疗,皮疹在发病后 7 天内消退。认识到这种情况及其良性性质可以使患者免于进行广泛的检查,并减轻患者家属和医护人员的焦虑。

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引用本文的文献

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Köbner and Pastia Signs in Acute Hemorrhagic Edema of Young Children: Systematic Literature Review.儿童急性出血性水肿中的科布纳征和帕斯蒂亚征:系统文献综述
Children (Basel). 2022 Feb 15;9(2):265. doi: 10.3390/children9020265.

本文引用的文献

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Acute Hemorrhagic Edema of Infancy.婴儿急性出血性水肿
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Acute hemorrhagic edema of young children: a prospective case series.小儿急性出血性水肿:一项前瞻性病例系列研究。
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Target-shaped edematous purple lesions: is it child abuse?靶形水肿性紫色病变:是虐待儿童吗?
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