Brock Cameron L, Sharma Apoorva, Villada Fabio A, Schubert Johanna
Department of Radiology, CHI Creighton University Medical Center-Bergan Mercy, 7500 Mercy Rd, Omaha, NE 68124.
Department of Pathology, CHI Creighton University Medical Center-Bergan Mercy, 7500 Mercy Rd, Omaha, NE 68124.
Radiol Case Rep. 2020 Oct 28;16(1):18-21. doi: 10.1016/j.radcr.2020.10.010. eCollection 2021 Jan.
Ganglioneuromas (GN) are rare, mature tumors that arise in the posterior mediastinum or retroperitoneum from neural crest cells and present as slow growing masses in the pediatric population. While they are often found incidentally in unrelated diagnostic workup, they can become symptomatic due to their size and location. They typically demonstrate the nonspecific appearance of a solid mass without invasive or destructive features across different modalities. Such features are normally indicative of more aggressive neoplasms from similar cellular ancestry or an entirely different lineage. Here we present a case of mediastinal GN that on imaging was initially suggestive of an osteochondroma with malignant degeneration based on the presence of an exostosis associated with a large solid mass. Final pathology, however, revealed GN with involvement of the adjacent bone. While the final diagnosis was benign, it is important to recognize this pattern of exostosis with solid mass, especially since the overall survival rate of sarcomata is much worse than that of a classic GN.
神经节神经瘤(GN)是一种罕见的成熟肿瘤,起源于神经嵴细胞,发生于后纵隔或腹膜后,在儿童群体中表现为生长缓慢的肿块。虽然它们常在无关的诊断检查中偶然发现,但因其大小和位置可能会出现症状。在不同检查方式下,它们通常表现为实性肿块的非特异性外观,无侵袭性或破坏性特征。这些特征通常提示来自相似细胞谱系或完全不同谱系的更具侵袭性的肿瘤。在此,我们报告一例纵隔GN病例,该病例在影像学上最初因存在与大实性肿块相关的外生骨疣而提示为伴有恶性变的骨软骨瘤。然而,最终病理显示为GN并累及相邻骨骼。虽然最终诊断为良性,但认识到这种伴有实性肿块的外生骨疣模式很重要,特别是因为肉瘤的总体生存率远低于经典GN。