Department of Medical Informatics, College of Medicine, The Catholic University of Korea, Seoul, Korea.
Cancer Research Institute, College of Medicine, The Catholic University of Korea, 222 Banpo-daero, Seocho-Gu, Seoul, 06591, Republic of Korea.
Sci Rep. 2020 Nov 11;10(1):19555. doi: 10.1038/s41598-020-76510-7.
Allogeneic stem cell transplantation is currently the only curative treatment option for myelodysplastic syndromes (MDS). Pre-transplant debulking treatment have been employed for advanced MDS and we previously reported that marrow response (blast ≤ 5%) following the bridging therapy with hypomethylating agent was an independent favorable factor for survival; however, it is still not clear which patients will respond to hypomethylating agent and which genomic features can predict the response. In this study, we performed RNAseq for 23 MDS patients among which 14 (61%) and 9 (39%) patients showed marrow complete remission and primary resistance to azacitidine, respectively. Differential expression-based analyses of treatment-naive, baseline gene expression profiles revealed that molecular functions representing mitochondria and apoptosis were up-regulated in responders. In contrast, we identified genes involved in the Wnt pathway were relatively up-regulated in non-responders. In independent validation cohorts of MDS patients, the expression of gene sets specific to non-responders and responders distinguished the patients with favorable prognosis and those responded to azacitidine highlighting the prognostic and predictive implication. In addition, a systems biology approach identified genes involved in ubiquitination, such as UBC and PFDN2, which may be key players in the regulation of differential gene expression in treatment responders and non-responders. Taken together, identifying the gene expression signature may advance our understanding of the molecular mechanisms of azacitidine and may also serve to predict patient responses to drug treatment.
异基因造血干细胞移植是目前治疗骨髓增生异常综合征(MDS)的唯一根治方法。对于晚期 MDS,我们采用移植前减瘤治疗,我们之前报道过,桥接治疗使用低甲基化药物后骨髓反应(原始细胞 ≤ 5%)是生存的独立有利因素;然而,目前仍不清楚哪些患者对低甲基化药物有反应,哪些基因组特征可以预测反应。在这项研究中,我们对 23 名 MDS 患者进行了 RNAseq 分析,其中 14 名(61%)和 9 名(39%)患者分别出现骨髓完全缓解和阿扎胞苷原发性耐药。对治疗前、基线基因表达谱的差异表达分析显示,代表线粒体和细胞凋亡的分子功能在应答者中上调。相比之下,我们发现非应答者中相对上调的基因涉及 Wnt 通路。在独立的 MDS 患者验证队列中,非应答者和应答者特有的基因集的表达区分了预后良好和对阿扎胞苷有反应的患者,突出了其预后和预测意义。此外,系统生物学方法鉴定了参与泛素化的基因,如 UBC 和 PFDN2,它们可能是治疗应答者和非应答者差异基因表达调控的关键参与者。总之,鉴定基因表达谱可能有助于我们深入了解阿扎胞苷的分子机制,并可用于预测患者对药物治疗的反应。