Jørgensen J S, Guthoff R
Univ.-Augenklinik, Rigshospitalet, Kopenhagen.
Klin Monbl Augenheilkd. 1987 Oct;191(4):275-8. doi: 10.1055/s-2008-1050508.
The present report describes clinical findings in 13 patients with Sturge-Weber syndrome, 11 of whom had glaucoma (22-52 mm Hg). The episcleral venous pressure (EVP) was high in all glaucomatous eyes (14-23 mm Hg). Tonography showed a marked decrease in outflow facility. The observations suggest that glaucoma in Sturge-Weber syndrome is caused by a) elevated episcleral venous pressure and b) secondary damage of the trabecular meshwork with reduction of outflow facility. The cause and pathogenesis of these lesions are discussed. In nine patients a diffuse angiomatosis involving most of the choroid (1.5-4.0 mm thick), as well as the episcleral perilimbal plexus, was demonstrated by ultrasonography.
本报告描述了13例斯特奇-韦伯综合征患者的临床发现，其中11例患有青光眼（眼压22 - 52毫米汞柱）。所有青光眼患眼的巩膜静脉压（EVP）均升高（14 - 23毫米汞柱）。眼压描记显示房水流畅系数显著降低。这些观察结果表明，斯特奇-韦伯综合征中的青光眼是由以下原因引起的：a）巩膜静脉压升高；b）小梁网继发性损伤导致房水流畅系数降低。文中讨论了这些病变的病因和发病机制。通过超声检查发现，9例患者存在累及大部分脉络膜（厚度为1.5 - 4.0毫米）以及巩膜周边角膜缘丛的弥漫性血管瘤病。
