Department of Medical Oncology, Faculty of Medicine of Tunis, University of Tunis El Manar, Military Hospital of Tunis, Montfleury, Tunis, Tunisia.
Department of Pathology, Faculty of Medicine of Tunis, University of Tunis El Manar, Military Hospital of Tunis, Montfleury, Tunis, Tunisia.
Pan Afr Med J. 2020 Sep 15;37:59. doi: 10.11604/pamj.2020.37.59.24836. eCollection 2020.
Chordoma is a rare malignant tumor of the spine. We report the case of a 26-year-old man who presented with facial paralysis and upper limbs paresthesia. Cerebral CT-scan and cerebro-spinal MRI revealed a 58mm locally advanced middle clival mass with deviation of median cerebral structures. Endoscopic biopsy concluded to a chondroid chordoma. Skeletal survey and thoraco-abdomino-pelvic CT-scan were normal. Treatment consisted in complete surgical removal of the tumor followed by adjuvant radiotherapy. The patient is alive free of disease with a follow up of 12 months.
脊索瘤是一种罕见的脊柱恶性肿瘤。我们报告了 1 例 26 岁男性患者，表现为面瘫和上肢感觉异常。颅脑 CT 扫描和脑脊髓 MRI 显示 58mm 局部晚期鞍区肿块，伴有中线脑结构偏斜。内镜活检提示软骨样脊索瘤。全身骨骼扫描和胸腹盆 CT 扫描正常。治疗包括完全切除肿瘤，然后辅助放疗。患者在随访 12 个月时无疾病生存。
