Ahmed Jawwad, Saqulain Ghulam, Khan Muhammad Iqbal Javed, Kausar Mobeen
Dr. Jawwad Ahmed, FCPS (Otolaryngology), Associate Surgeon, Department of Otolaryngology & Cochlear Implantation, Capital Hospital PGMI, Islamabad, Pakistan.
Dr. Ghulam Saqulain, FCPS (Otorhinolaryngology), Head of Department of Otorhinolaryngology & Cochlear Implantation, Capital Hospital PGMI, CDA, Islamabad, Pakistan.
Pak J Med Sci. 2020 Nov-Dec;36(7):1511-1516. doi: 10.12669/pjms.36.7.3134.
To determine the prevalence and features of inner ear anomalies in children with congenital profound hearing loss who presented at our cochlear implant center based on imaging studies.
This retrospective study reviewed charts of children with congenital SNHL, who presented to Department of Otolaryngology & Auditory Implant Centre, Capital Hospital Islamabad over a period of 2 years from 1 May 2017 to 30 April 2019. These included 481 cases of both genders aged between 1 to 12 years. After gathering demographic data, audiological data, computed tomography findings of the temporal bone were analyzed. Data was analyzed using SPSS 22.
The Inner Ear Malformations were identified in 48(10%) children including 28 (58.33%) males and 20 (41.67%) female. Most 20(41.67%) presented at >3-5 years of age followed by 19(39.58%) at 2-3 years. However, no significant association of gender (p=0.57, p=0.076) and age of presentation (p=0.344, p=0.697) for right and left ears was noted with inner ear malformations. The most common anomaly noted were CLA, CH-III and CH-II in decreasing order of frequency in both ears.
The prevalence of IEM's was found to be 48(10%). Commonest anomalies noted were CLA, CH-III and CH-II. No significant association of gender and age of presentation was noted with type of anomaly in both ears.
基于影像学研究，确定在我们的人工耳蜗植入中心就诊的先天性重度听力损失儿童内耳异常的患病率及特征。
这项回顾性研究对2017年5月1日至2019年4月30日期间在伊斯兰堡首都医院耳鼻喉科及听觉植入中心就诊的先天性感音神经性听力损失儿童的病历进行了回顾。其中包括481例年龄在1至12岁之间的男女患儿。收集人口统计学数据、听力学数据后，对颞骨的计算机断层扫描结果进行分析。使用SPSS 22软件进行数据分析。
48名（10%）儿童被确诊为内耳畸形，其中男性28名（58.33%），女性20名（41.67%）。大多数患儿（20名，41.67%）在3至5岁以上就诊，其次是19名（39.58%）在2至3岁就诊。然而，未发现内耳畸形与左右耳的性别（p=0.57，p=0.076）及就诊年龄（p=0.344，p=0.697）之间存在显著关联。双耳中最常见的异常依次为共同腔畸形、耳蜗发育不全III型和耳蜗发育不全II型。
内耳畸形的患病率为48例（10%）。最常见的异常为共同腔畸形、耳蜗发育不全III型和耳蜗发育不全II型。未发现双耳异常类型与性别及就诊年龄之间存在显著关联。
