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酷似脉络膜黑色素瘤的巨大脉络膜黑素细胞瘤:一项困难的鉴别诊断及不可避免的眼球摘除术

Large Choroidal Melanocytoma Simulating Choroidal Melanoma: A Difficult Differential Diagnosis and an Inevitable Enucleation.

作者信息

Abdellaoui Taoufik, Belfaiza Soukaina, Malek Yassine, Essaoudi Mohamed-Amine, Elasri Fouad, Reda Karim, Oubaaz Abdelbarre

机构信息

Department of Ophthalmology, Military Teaching Hospital Med-V, Rabat, Morocco.

Department of Pathology, Military Teaching Hospital Med-V, Rabat, Morocco.

出版信息

Case Rep Ophthalmol Med. 2020 Nov 21;2020:8890857. doi: 10.1155/2020/8890857. eCollection 2020.

DOI:10.1155/2020/8890857
PMID:33294243
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7700045/
Abstract

PURPOSE

To describe a case of choroidal melanocytoma mimicking a melanoma.

METHODS

Retrospective case report. . A 48-year-old Moroccan woman presented with progressive, painless decreased vision in her left eye for 2 months.

RESULTS

Her visual acuity was light perception in the left eye and 20/20 in the right one. Fundus examination and fluorescein angiography of the left eye showed a total retinal detachment with a large superior brownish mass. The clinical examination, B-scan ultrasonography, and magnetic resonance imaging all suggested a malignant melanoma. Consequently, the eye was enucleated. The histopathology later revealed a benign melanocytoma of the choroid. . Melanocytoma is a rare benign pigmented tumor. It is classically described as a tumor of the optic nerve head, but there are some exceptional case reports of uveal tract locations (iris, ciliary body, and choroid). In such cases, it can be difficult to clinically differentiate a melanocytoma from a malignant melanoma.

摘要

目的

描述一例疑似黑色素瘤的脉络膜黑色素细胞瘤病例。

方法

回顾性病例报告。一名48岁摩洛哥女性,左眼渐进性、无痛性视力下降2个月。

结果

她的左眼视力为光感,右眼视力为20/20。左眼眼底检查和荧光素血管造影显示全视网膜脱离,上方有一个大的褐色肿块。临床检查、B超超声检查和磁共振成像均提示为恶性黑色素瘤。因此,该眼被摘除。组织病理学检查后来显示为脉络膜良性黑色素细胞瘤。黑色素细胞瘤是一种罕见的良性色素性肿瘤。经典描述为视神经乳头肿瘤,但也有一些关于葡萄膜部位(虹膜、睫状体和脉络膜)的特殊病例报告。在这种情况下,临床上很难将黑色素细胞瘤与恶性黑色素瘤区分开来。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b5f/7700045/add41a26fa25/CRIOPM2020-8890857.004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b5f/7700045/055897d3a054/CRIOPM2020-8890857.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b5f/7700045/f910604df53f/CRIOPM2020-8890857.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b5f/7700045/b387d50b256b/CRIOPM2020-8890857.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b5f/7700045/add41a26fa25/CRIOPM2020-8890857.004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b5f/7700045/055897d3a054/CRIOPM2020-8890857.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b5f/7700045/f910604df53f/CRIOPM2020-8890857.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b5f/7700045/b387d50b256b/CRIOPM2020-8890857.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b5f/7700045/add41a26fa25/CRIOPM2020-8890857.004.jpg

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